STRA6

signaling receptor and transporter of retinol STRA6

Summary

The protein encoded by this gene is a membrane protein involved in the metabolism of retinol. The encoded protein acts as a receptor for retinol/retinol binding protein complexes. This protein removes the retinol from the complex and transports it across the cell membrane. Defects in this gene are a cause of syndromic microphthalmia type 9 (MCOPS9). Several transcript variants encoding a few different isoforms have been found for this gene. [provided by RefSeq, Dec 2008]

Known Variants248 total

rsidPosition (GRCh37)AllelesClassClinVar
rs6200571015:74,471,793C/Tlikely benign
rs207287463515:74,471,839A/Guncertain significance
rs7829926215:74,471,852A/Gbenign
rs7511752415:74,471,932A/Gbenign
rs53390964715:74,471,995C/Tuncertain significance
rs55546977815:74,472,022C/Tuncertain significance
rs54474827115:74,472,040G/Auncertain significance
rs105223388015:74,472,053C/Guncertain significance
rs75766608815:74,472,097G/Auncertain significance
rs1091015:74,472,199T/Cbenign
rs88605147115:74,472,212C/Guncertain significance
rs19149690915:74,472,231G/Auncertain significance
rs52908773515:74,472,232C/Auncertain significance
rs74618962915:74,472,243G/Auncertain significance
rs207289090215:74,472,280C/Tuncertain significance
rs1163194415:74,472,294A/Gbenign
rs56731760415:74,472,316C/Tuncertain significance
rs88605147215:74,472,332A/Guncertain significance
rs18252952415:74,472,346G/Tlikely benign
rs102945920715:74,472,349G/Auncertain significance
rs88605147315:74,472,389C/Auncertain significance
rs54530988215:74,472,411T/Guncertain significance
rs14707771615:74,472,424G/Alikely benign
rs77530973115:74,472,433A/Guncertain significance
rs14404330415:74,472,455G/Auncertain significance
rs39751463915:74,472,461C/Tmissense variantpathogenic
rs11820395915:74,472,462G/Amissense variantpathogenic
rs15068741115:74,472,468C/Tuncertain significance
rs207290226415:74,472,483T/Guncertain significance
rs155545344415:74,472,490C/Tuncertain significance
rs11820396015:74,472,494G/Amissense variantpathogenic
rs250574038115:74,472,503A/Tuncertain significance
rs156717575715:74,472,508C/Tuncertain significance
rs14469144515:74,472,512C/Gmissense variantpathogenic
rs77520079115:74,472,513G/Auncertain significance
rs14561461215:74,472,522T/Clikely benign
rs20017861615:74,472,525G/Auncertain significance
rs14430838815:74,472,534C/Tlikely benign
rs250574090615:74,472,545C/Tuncertain significance
rs74736813615:74,472,554A/Guncertain significance
rs78175735615:74,472,558A/Cuncertain significance
rs37195810615:74,472,577C/Guncertain significance
rs77304749615:74,472,596G/Alikely benign
rs35124215:74,472,716G/Abenign
rs488657815:74,473,035T/Cbenign
rs1291257815:74,473,073A/Gbenign
rs11805660615:74,473,111G/Alikely benign
rs77843077315:74,473,119G/Auncertain significance
rs20100832615:74,473,124T/Auncertain significance
rs14204881515:74,473,127G/Abenign
rs76524261215:74,473,146A/Cuncertain significance
rs37467638615:74,473,153C/Guncertain significance
rs227760715:74,473,160G/Alikely benign
rs11533176215:74,473,192C/Tlikely benign
rs37293189515:74,473,228G/Cmissense variantpathogenic
rs56038239315:74,473,249T/Auncertain significance
rs75086464115:74,473,264G/Alikely pathogenic
rs20048343415:74,473,269G/Auncertain significance
rs54898818515:74,473,270T/Cuncertain significance
rs75793148415:74,473,271G/Alikely benign
rs20173071715:74,473,283G/Cconflicting classifications of pathogenicity
rs15114842215:74,473,293C/Tbenign
rs1291304115:74,473,302A/Gbenign
rs14026905915:74,473,371T/Glikely benign
rs11205193415:74,473,391A/Tlikely benign
rs39751463815:74,473,642C/Gmissense variantpathogenic
rs20158261215:74,473,643G/Alikely benign
rs74828602415:74,473,650G/Auncertain significance
rs36888359515:74,473,651C/Tuncertain significance
rs37214967215:74,473,652G/Alikely benign
rs75988726315:74,473,659G/Auncertain significance
rs250575261715:74,473,689A/Guncertain significance
rs14100406715:74,473,715G/Auncertain significance
rs207297857615:74,473,725C/Auncertain significance
rs57021433615:74,473,726G/Apathogenic
rs73611815:74,473,739T/Cbenign
rs88605147415:74,473,754C/Aconflicting classifications of pathogenicity
rs55904253015:74,473,755A/Cuncertain significance
rs39751848415:74,473,800C/Tpathogenic
rs1185566715:74,474,010A/Cbenign
rs7596649915:74,474,083T/Cbenign
rs7628614115:74,474,302C/Tlikely benign
rs20060908015:74,474,488A/Guncertain significance
rs75147796415:74,474,502C/Tuncertain significance
rs37667887915:74,474,503G/Auncertain significance
rs156717820415:74,474,504G/Tuncertain significance
rs14335069715:74,474,582G/Alikely benign
rs124932622015:74,474,612G/Tlikely benign
rs19950887815:74,474,614G/Alikely benign
rs207303436315:74,474,666A/Clikely benign
rs35124115:74,474,686C/Tlikely benign
rs20140842515:74,474,711A/Clikely benign
rs75314427015:74,474,725A/Guncertain significance
rs74874338215:74,474,753G/Tuncertain significance
rs36807301815:74,474,761C/Tuncertain significance
rs250576316215:74,474,765G/Cuncertain significance
rs86902526915:74,474,789T/Cmissense variantpathogenic
rs136721526815:74,474,807A/Tpathogenic
rs7951042615:74,474,813G/Alikely benign
rs35124015:74,474,845T/Gupstream gene variant

Showing 100 of 248 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.