SYT14

synaptotagmin 14

Summary

This gene is a member of the synaptotagmin gene family and encodes a protein similar to other family members that mediate membrane trafficking in synaptic transmission. The encoded protein is a calcium-independent synaptotagmin. Mutations in this gene are a cause of autosomal recessive spinocerebellar ataxia-11 (SCAR11), and a t(1;3) translocation of this gene has been associated with neurodevelopmental abnormalities. Alternatively spliced transcript variants encoding multiple isoforms have been observed for this gene, and a pseudogene of this gene is located on the long arm of chromosome 4. [provided by RefSeq, Dec 2011]

Known Variants80 total

rsidPosition (GRCh37)AllelesClassClinVar
rs66921161:210,111,242A/Tbenign
rs1399947211:210,111,493C/Tbenign
rs5429124821:210,111,546C/Tlikely benign
rs3685454521:210,111,597T/Cuncertain significance
rs7491928021:210,111,605G/Alikely benign
rs9852323901:210,111,607A/Gconflicting classifications of pathogenicity
rs13517590001:210,111,617T/Clikely benign
rs15532557751:210,111,623G/Alikely pathogenic
rs120251141:210,111,733A/Gbenign
rs75309071:210,125,880T/Cbenign
rs5670637871:210,126,082A/Guncertain significance
rs107795181:210,139,069G/Abenign
rs20791499121:210,139,243G/Tuncertain significance
rs8664401021:210,139,277A/Guncertain significance
rs9146592491:210,139,302G/Auncertain significance
rs98036201:210,139,506C/Tbenign
rs121365401:210,155,962T/Cintron variant
rs1499328521:210,187,034C/Auncertain significance
rs1889952201:210,187,037C/Tuncertain significance
rs15721582451:210,187,108A/Glikely benign
rs1491702801:210,187,118A/Guncertain significance
rs5651848771:210,194,202A/Gbenign
rs15532670671:210,194,429G/Auncertain significance
rs9782168361:210,194,431G/Auncertain significance
rs1419745171:210,194,442G/Alikely benign
rs7464054531:210,194,524T/Cuncertain significance
rs11927753881:210,194,549C/Guncertain significance
rs1459635111:210,194,555C/Tconflicting classifications of pathogenicity
rs1165931361:210,194,556G/Abenign
rs715151481:210,194,565T/Clikely benign
rs111193941:210,194,685A/Glikely benign
rs2271791:210,216,731A/Gintron variant
rs2272061:210,241,985T/Gintron variant
rs350463991:210,255,765T/Cintron variant
rs2271991:210,265,384G/Cintron variant
rs25279075971:210,267,670A/Guncertain significance
rs1451677601:210,267,753C/Tbenign
rs10271153431:210,267,775T/Cuncertain significance
rs2000870651:210,267,811A/Guncertain significance
rs11598950351:210,267,935T/Clikely benign
rs5340944791:210,273,354T/Cbenign
rs7492557671:210,273,416A/Cuncertain significance
rs1495449141:210,273,523G/Auncertain significance
rs15722976441:210,273,578A/Glikely benign
rs25279438311:210,273,676T/Guncertain significance
rs8678869511:210,273,696C/Tuncertain significance
rs1428535301:210,273,697G/Alikely benign
rs3765099521:210,273,710A/Glikely benign
rs15722981311:210,273,773G/Alikely benign
rs2012253421:210,273,783T/Clikely benign
rs24941871:210,273,886A/Tbenign
rs48449471:210,302,700G/Cintron variant
rs75168431:210,322,929A/Gintron variant
rs45891091:210,328,813G/Tbenign
rs7592255291:210,329,083G/Auncertain significance
rs7521966111:210,329,085G/Auncertain significance
rs1922580591:210,329,087G/Alikely benign
rs20832568851:210,329,140T/Auncertain significance
rs25282326201:210,329,202C/Tuncertain significance
rs13751437211:210,329,216G/Auncertain significance
rs3879070331:210,329,217G/Amissense variantpathogenic
rs124085411:210,332,577C/Alikely benign
rs9271301911:210,332,757T/Clikely benign
rs25282516501:210,332,777T/Cuncertain significance
rs75350451:210,333,776A/Gbenign
rs730617321:210,333,943C/Tlikely benign
rs171881831:210,334,081C/Tbenign
rs13330751041:210,334,106A/Guncertain significance
rs15723981561:210,334,109G/Auncertain significance
rs7462789651:210,334,155C/Guncertain significance
rs7683441451:210,334,198A/Glikely benign
rs170156951:210,334,201T/Cbenign
rs25282608171:210,334,226C/Guncertain significance
rs20833626151:210,334,311A/Guncertain significance
rs13696506621:210,334,317A/Guncertain significance
rs12550719361:210,334,363A/Cuncertain significance
rs9707965381:210,334,371C/Tuncertain significance
rs3717890981:210,334,372G/Alikely benign
rs14825169411:210,334,386G/Auncertain significance
rs785080491:210,344,884T/A

Gene information from NCBI Gene. Variant classifications from ClinVar.