TBC1D5

TBC1 domain family member 5

Summary

Enables AP-2 adaptor complex binding activity and retromer complex binding activity. Involved in several processes, including macroautophagy; positive regulation of receptor internalization; and retrograde transport, endosome to Golgi. Located in several cellular components, including Atg1/ULK1 kinase complex; autophagosome; and cytoplasmic vesicle membrane. Part of retromer complex. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants33 total

rsidPosition (GRCh37)AllelesClassClinVar
rs7580516453:17,202,505C/Tuncertain significance
rs2008327253:17,202,706C/Tuncertain significance
rs7743915193:17,208,302C/Tuncertain significance
rs1392103703:17,208,341G/Tlikely benign
rs1467915493:17,208,352C/Guncertain significance
rs3699423333:17,208,366C/Tuncertain significance
rs5653774803:17,209,278T/Cuncertain significance
rs1492154043:17,226,601C/Glikely benign
rs1433655713:17,226,606T/Cuncertain significance
rs9949772683:17,226,639A/Tuncertain significance
rs25474309683:17,226,672A/Guncertain significance
rs7500357253:17,255,800A/Tuncertain significance
rs1396033423:17,255,827C/Tlikely benign
rs25483065253:17,275,196C/Guncertain significance
rs7567115573:17,275,242C/Tuncertain significance
rs25483771913:17,279,670C/Tuncertain significance
rs9233879373:17,279,726T/Cuncertain significance
rs27334813:17,320,397G/Aintron variant
rs25494215383:17,333,403A/Guncertain significance
rs10270535153:17,333,410C/Tuncertain significance
rs7749475003:17,333,467G/Cuncertain significance
rs3757499093:17,349,615C/Tuncertain significance
rs98707413:17,407,930T/A
rs2017690453:17,413,575T/Cuncertain significance
rs1418510703:17,415,967T/Cuncertain significance
rs5473942803:17,416,010C/Guncertain significance
rs7522868733:17,425,468T/Guncertain significance
rs7523000253:17,444,698T/Cuncertain significance
rs20937259693:17,446,235A/Guncertain significance
rs344577483:17,446,447G/Alikely benign
rs76281263:17,520,888C/Glikely benign
rs7659186213:17,550,014G/Cuncertain significance
rs1838362883:17,664,509A/Gintron variant

Gene information from NCBI Gene. Variant classifications from ClinVar.