TIE1

tyrosine kinase with immunoglobulin like and EGF like domains 1

Summary

This gene encodes a member of the tyrosine protein kinase family. The encoded protein plays a critical role in angiogenesis and blood vessel stability by inhibiting angiopoietin 1 signaling through the endothelial receptor tyrosine kinase Tie2. Ectodomain cleavage of the encoded protein relieves inhibition of Tie2 and is mediated by multiple factors including vascular endothelial growth factor. Alternatively spliced transcript variants encoding multiple isoforms have been observed for this gene. [provided by RefSeq, Nov 2011]

Known Variants93 total

rsidPosition (GRCh37)AllelesClassClinVar
rs1399077841:43,766,753G/Auncertain significance
rs9369485221:43,766,761C/Guncertain significance
rs25456228301:43,770,576G/Tuncertain significance
rs7608027721:43,770,671G/Auncertain significance
rs14703981071:43,770,678C/Auncertain significance
rs7515607771:43,770,686G/Auncertain significance
rs3773151791:43,770,720A/Tuncertain significance
rs7565750491:43,770,737G/Auncertain significance
rs16467130191:43,770,741T/Guncertain significance
rs12723674641:43,770,803A/Guncertain significance
rs7569239171:43,770,813T/Cuncertain significance
rs11959940221:43,770,964C/Guncertain significance
rs7751698201:43,770,985A/Guncertain significance
rs2018016181:43,771,013C/Tbenign
rs740695511:43,771,880G/Aintron variant
rs12510808351:43,772,528C/Guncertain significance
rs1513252231:43,772,550A/Tuncertain significance
rs3754486081:43,772,555C/Tuncertain significance
rs1504069821:43,772,556G/Auncertain significance
rs1839103551:43,772,592C/Tuncertain significance
rs1381897241:43,772,597G/Auncertain significance
rs7525578681:43,772,642G/Auncertain significance
rs7581946631:43,772,651C/Tuncertain significance
rs5733418751:43,772,663C/Tuncertain significance
rs1450466521:43,772,664G/Auncertain significance
rs340846031:43,772,665G/Abenign
rs7537060881:43,772,827C/Tuncertain significance
rs7583408601:43,772,835G/Tlikely benign
rs350330631:43,772,886C/Tbenign
rs5495858661:43,772,899G/Auncertain significance
rs5694407371:43,772,932C/Tuncertain significance
rs7482124421:43,773,165C/Tuncertain significance
rs1404785591:43,773,166G/Auncertain significance
rs7539321501:43,773,500G/Auncertain significance
rs1443774581:43,774,711C/Tuncertain significance
rs1997157341:43,774,719C/Tuncertain significance
rs5602793911:43,774,797C/Tuncertain significance
rs22822261:43,774,878C/A
rs14678790421:43,775,104G/Auncertain significance
rs9918794611:43,775,131A/Tuncertain significance
rs7671533031:43,775,167G/Cuncertain significance
rs3765495151:43,775,179C/Tuncertain significance
rs5322520971:43,775,180G/Auncertain significance
rs16467678851:43,775,191G/Auncertain significance
rs1817169291:43,775,197G/Auncertain significance
rs563027941:43,777,350G/Auncertain significance
rs3759169151:43,777,408C/Tuncertain significance
rs1401906281:43,777,417C/Tmissense variant
rs1392444001:43,777,449C/Tpathogenic
rs13799373301:43,777,453T/Cuncertain significance
rs7548224831:43,777,712G/Cuncertain significance
rs1416280491:43,777,725G/Auncertain significance
rs5401629521:43,777,767G/Tuncertain significance
rs9362800671:43,778,017G/Auncertain significance
rs3768606901:43,778,077G/Auncertain significance
rs1446998701:43,778,122C/Tuncertain significance
rs7577632801:43,778,159C/Tuncertain significance
rs14565002721:43,778,164C/Guncertain significance
rs3678901411:43,778,254G/Auncertain significance
rs7776634961:43,778,821G/Auncertain significance
rs7572447491:43,778,832G/Auncertain significance
rs1995655951:43,778,866C/Tuncertain significance
rs1496313841:43,778,878C/Tuncertain significance
rs7662207951:43,778,882G/Cuncertain significance
rs11797437881:43,778,909C/Tlikely benign
rs7807190921:43,778,935G/Tuncertain significance
rs1408962721:43,778,988A/Guncertain significance
rs2006686801:43,778,994C/Tuncertain significance
rs7798401011:43,779,006G/Auncertain significance
rs16468208761:43,779,020C/Tlikely benign
rs3760141761:43,779,033C/Tuncertain significance
rs7637488771:43,779,481C/Tuncertain significance
rs25456443901:43,779,487G/Auncertain significance
rs1428356821:43,779,534C/Tbenign
rs7645883971:43,779,613C/Tuncertain significance
rs12917437721:43,779,614G/Tuncertain significance
rs29919901:43,779,869T/Gintron variant
rs14191565731:43,782,871G/Auncertain significance
rs5498891831:43,782,919G/Auncertain significance
rs1393581141:43,782,957G/Alikely benign
rs7703081111:43,782,987G/Auncertain significance
rs1433180721:43,783,021T/Guncertain significance
rs25456509701:43,783,037G/Cuncertain significance
rs7505373041:43,783,268C/Tuncertain significance
rs14471445641:43,783,619G/Auncertain significance
rs5658438411:43,783,649G/Auncertain significance
rs7613019141:43,785,018T/Cuncertain significance
rs3746035041:43,786,969T/Cuncertain significance
rs1467996671:43,787,301G/Auncertain significance
rs9487192311:43,787,318C/Tuncertain significance
rs349932021:43,787,367G/Apathogenic
rs25456620501:43,788,321G/Cuncertain significance
rs25456621171:43,788,361G/Cuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.