TNFRSF1B

TNF receptor superfamily member 1B

Summary

The protein encoded by this gene is a member of the TNF-receptor superfamily. This protein and TNF-receptor 1 form a heterocomplex that mediates the recruitment of two anti-apoptotic proteins, c-IAP1 and c-IAP2, which possess E3 ubiquitin ligase activity. The function of IAPs in TNF-receptor signalling is unknown, however, c-IAP1 is thought to potentiate TNF-induced apoptosis by the ubiquitination and degradation of TNF-receptor-associated factor 2, which mediates anti-apoptotic signals. Knockout studies in mice also suggest a role of this protein in protecting neurons from apoptosis by stimulating antioxidative pathways. [provided by RefSeq, Jul 2008]

Known Variants32 total

rsidPosition (GRCh37)AllelesClassClinVar
rs6526251:12,225,351T/Aupstream gene variant
rs9768811:12,233,754T/Cregulatory region variant
rs5190641:12,242,096C/Tintron variant
rs767691201:12,243,825G/Tintron variant
rs14206872441:12,248,854T/Cuncertain significance
rs12627536881:12,248,912T/Clikely benign
rs57460111:12,250,004T/Cregulatory region variant
rs57460171:12,251,341A/Cregulatory region variant
rs7564272481:12,252,527C/Guncertain significance
rs22754151:12,252,573C/Tbenign
rs22284941:12,252,927G/Abenign
rs10616221:12,252,955T/Gmissense variantuncertain significance
rs10352187721:12,252,970C/Guncertain significance
rs1998730501:12,252,976C/Tbenign
rs25236757421:12,253,038T/Cuncertain significance
rs16391837991:12,253,066C/Auncertain significance
rs1469833801:12,253,136C/Tlikely benign
rs5518665271:12,253,162C/Alikely benign
rs22297001:12,254,015T/Cbenign
rs1999316401:12,262,042A/Gbenign
rs5341149571:12,262,048C/Tuncertain significance
rs25237124931:12,262,078C/Guncertain significance
rs2018720771:12,262,095G/Clikely benign
rs16394067421:12,262,164G/Cuncertain significance
rs7482611321:12,262,185G/Cuncertain significance
rs9714042331:12,262,207C/Tuncertain significance
rs57460591:12,262,792A/T
rs25237322711:12,266,974G/Auncertain significance
rs13896813971:12,266,994G/Auncertain significance
rs10616241:12,267,265A/T
rs33971:12,267,292C/T3 prime UTR variantuncertain significance
rs10616311:12,268,499G/A3 prime UTR variant

Gene information from NCBI Gene. Variant classifications from ClinVar.