TRHR

thyrotropin releasing hormone receptor

Summary

This gene encodes a G protein-coupled receptor for thyrotropin-releasing hormone (TRH). Upon binding to TRH, this receptor activates the inositol phospholipid-calcium-protein kinase C transduction pathway. Mutations in this gene have been associated with generalized thyrotropin-releasing hormone resistance. [provided by RefSeq, Sep 2011]

Known Variants26 total

rsidPosition (GRCh37)AllelesClassClinVar
rs57728:110,098,632G/Cupstream gene variant
rs2020862298:110,099,750C/Tbenign
rs7467255888:110,099,776C/Tuncertain significance
rs1219178478:110,099,790C/Tstop gainedpathogenic
rs57758:110,099,864A/Gbenign
rs9085198518:110,099,892A/Cuncertain significance
rs7542881928:110,099,973G/Auncertain significance
rs15861828378:110,099,983C/Glikely pathogenic
rs3722833178:110,100,031G/Cuncertain significance
rs3768322628:110,100,042A/Guncertain significance
rs7608237178:110,100,120A/Glikely benign
rs7712223498:110,100,133T/Cpathogenic
rs25369061598:110,100,173G/Cuncertain significance
rs1507196398:110,100,230G/Alikely benign
rs7789873698:110,100,274C/Auncertain significance
rs25369064558:110,100,418A/Cuncertain significance
rs7692200338:110,100,449T/Clikely benign
rs31341128:110,104,855A/C
rs168924968:110,109,851A/T
rs78214638:110,112,887A/T
rs78325528:110,115,676C/Tintron variant
rs126800288:110,123,183C/A
rs18119649418:110,131,415T/Cuncertain significance
rs7504233108:110,131,512C/Tuncertain significance
rs1470192358:110,131,553G/Alikely benign
rs57768:110,131,636T/Cbenign

Gene information from NCBI Gene. Variant classifications from ClinVar.