TSC1

TSC complex subunit 1

Summary

This gene is a tumor suppressor gene that encodes the growth inhibitory protein hamartin. The encoded protein interacts with and stabilizes the GTPase activating protein tuberin. This hamartin-tuberin complex negatively regulates mammalian target of rapamycin complex 1 (mTORC1) signaling which is a major regulator of anabolic cell growth. This protein also functions as a co-chaperone for Hsp90 that inhibits its ATPase activity. This protein functions as a facilitator of Hsp90-mediated folding of kinase and non-kinase clients, including TSC2 and thereby preventing their ubiquitination and proteasomal degradation. Mutations in this gene have been associated with tuberous sclerosis and lymphangioleiomyomatosis. [provided by RefSeq, May 2022]

Known Variants2,993 total

rsidPosition (GRCh37)AllelesClassClinVar
rs792207159:135,766,724C/Tbenign
rs8860635629:135,766,777C/Auncertain significance
rs8860635639:135,766,796T/Guncertain significance
rs5763429259:135,766,834T/Gbenign
rs794700949:135,766,859A/Gbenign
rs7479699329:135,766,942C/Aconflicting classifications of pathogenicity
rs8860635649:135,767,000C/Tuncertain significance
rs3975148219:135,767,031C/Anot provided
rs10368254179:135,767,084T/Cuncertain significance
rs9183385519:135,767,100G/Auncertain significance
rs8860635659:135,767,107C/Tuncertain significance
rs8894367089:135,767,130A/Guncertain significance
rs1129684929:135,767,175G/Auncertain significance
rs115537639:135,767,185C/Tbenign
rs5524535279:135,767,237C/Abenign
rs8860635669:135,767,266G/Auncertain significance
rs1398010349:135,767,368C/Tuncertain significance
rs8860635679:135,767,374G/Auncertain significance
rs8860635689:135,767,389C/Auncertain significance
rs8860635699:135,767,429T/Guncertain significance
rs8860635709:135,767,455G/Tuncertain significance
rs8860635719:135,767,463C/Auncertain significance
rs8860635729:135,767,494C/Tuncertain significance
rs18448020909:135,767,503A/Guncertain significance
rs15882769229:135,767,517G/Auncertain significance
rs8860635739:135,767,550C/Tuncertain significance
rs171498989:135,767,565T/Cbenign
rs1489829249:135,767,625C/Tuncertain significance
rs5638354849:135,767,634C/Tlikely benign
rs8860635749:135,767,635T/Cuncertain significance
rs14454396959:135,767,663A/Guncertain significance
rs1144541559:135,767,670T/Cbenign
rs3975148539:135,767,686G/Anot provided
rs3975147879:135,767,687G/Anot provided
rs8860635759:135,767,698C/Auncertain significance
rs5722310789:135,767,786C/Tuncertain significance
rs5758122239:135,767,789G/Tlikely benign
rs5449315389:135,767,792G/Aconflicting classifications of pathogenicity
rs8860635769:135,767,885G/Tuncertain significance
rs5433961729:135,767,893C/Abenign
rs18448268939:135,767,937C/Tuncertain significance
rs10507009:135,767,943C/Tbenign
rs8860635779:135,767,964C/Tuncertain significance
rs1133132029:135,767,974G/Auncertain significance
rs7714947839:135,768,057G/Auncertain significance
rs8860635789:135,768,079G/Tuncertain significance
rs5333248679:135,768,084T/Cbenign
rs8860635799:135,768,091C/Auncertain significance
rs13354231309:135,768,138T/Cuncertain significance
rs2010924669:135,768,174G/Abenign
rs5534753079:135,768,292C/Auncertain significance
rs8860635809:135,768,337C/Auncertain significance
rs8860635819:135,768,338G/Tuncertain significance
rs8669200239:135,768,350T/Cuncertain significance
rs3975147829:135,768,362C/Gnot provided
rs3975148779:135,768,364C/Gnot provided
rs8860635839:135,768,382C/Auncertain significance
rs8860635849:135,768,383C/Auncertain significance
rs8860635859:135,768,384A/Guncertain significance
rs3676058709:135,768,452C/Tuncertain significance
rs18448567939:135,768,530A/Guncertain significance
rs8860635869:135,768,559T/Auncertain significance
rs8860635879:135,768,575G/Tuncertain significance
rs7463653449:135,768,577T/Cuncertain significance
rs7642207039:135,768,588A/Guncertain significance
rs8860635889:135,768,673T/Auncertain significance
rs18448648839:135,768,698A/Guncertain significance
rs5599789989:135,768,718C/Aconflicting classifications of pathogenicity
rs8860635899:135,768,725T/Cuncertain significance
rs9467841369:135,768,732T/Cuncertain significance
rs1118328129:135,768,748C/Tbenign
rs21063459:135,768,750C/Tbenign
rs8997618829:135,768,768A/Guncertain significance
rs8860635919:135,768,793T/Cuncertain significance
rs735528059:135,768,889T/Cbenign
rs7495351359:135,768,898G/Auncertain significance
rs1504338099:135,768,914C/Gbenign
rs8860635929:135,768,931T/Auncertain significance
rs8860635939:135,768,943A/Guncertain significance
rs8860635949:135,768,964C/Auncertain significance
rs556609909:135,768,971A/Cbenign
rs8860635959:135,768,975G/Auncertain significance
rs8860635969:135,768,978C/Auncertain significance
rs3975148279:135,768,981C/Anot provided
rs3738453539:135,768,984G/Aconflicting classifications of pathogenicity
rs5388028389:135,768,985G/Cuncertain significance
rs8860635979:135,768,990T/Cuncertain significance
rs1898527689:135,768,994C/Gbenign
rs8860635989:135,769,007G/Tuncertain significance
rs8860635999:135,769,046A/Guncertain significance
rs1155161649:135,769,064T/Guncertain significance
rs8868785299:135,769,107A/Guncertain significance
rs8860636009:135,769,147G/Tuncertain significance
rs735528069:135,769,161C/Tbenign
rs5589667779:135,769,176T/Cuncertain significance
rs8860636019:135,769,183G/Tuncertain significance
rs1495875659:135,769,185C/Tbenign
rs1144151819:135,769,204C/Tbenign
rs8860636029:135,769,258A/Tuncertain significance
rs1148779819:135,769,268T/Cbenign

Showing 100 of 2,993 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.