TUBGCP2

tubulin gamma complex component 2

Summary

Predicted to enable gamma-tubulin binding activity. Predicted to contribute to microtubule minus-end binding activity. Involved in brain development and neuron migration. Located in centrosome; ciliary basal body; and nucleoplasm. Implicated in pachygyria, microcephaly, developmental delay, and dysmorphic facies, with or without seizures. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants129 total

rsidPosition (GRCh37)AllelesClassClinVar
rs137499275110:135,093,278C/Tuncertain significance
rs74925332410:135,093,279G/Alikely benign
rs18225217910:135,093,294G/Alikely benign
rs76345249010:135,093,307G/Aconflicting classifications of pathogenicity
rs89417209410:135,093,329C/Guncertain significance
rs54421414110:135,093,332G/Tuncertain significance
rs37233871910:135,093,376C/Tuncertain significance
rs76619515210:135,093,394T/Cuncertain significance
rs77636166610:135,094,787C/Tuncertain significance
rs20086769310:135,094,835G/Auncertain significance
rs20215129610:135,094,872G/Tuncertain significance
rs76946250110:135,094,895C/Tuncertain significance
rs37023087110:135,094,896G/Cuncertain significance
rs76750639610:135,095,735C/Tlikely benign
rs14791792510:135,095,750C/Tconflicting classifications of pathogenicity
rs56851107910:135,095,759C/Tuncertain significance
rs37369334810:135,095,762C/Auncertain significance
rs36783883810:135,095,817G/Auncertain significance
rs11239012010:135,095,851G/Tlikely benign
rs14174977210:135,096,591G/Abenign
rs184703090610:135,096,598A/Cuncertain significance
rs249359865310:135,096,663G/Alikely benign
rs54930591410:135,096,691G/Auncertain significance
rs14709681210:135,096,710C/Tuncertain significance
rs75265789110:135,096,732G/Alikely benign
rs14816084710:135,097,397T/Cuncertain significance
rs249360217910:135,097,415A/Tuncertain significance
rs74733359110:135,097,420G/Tuncertain significance
rs77122655210:135,097,433C/Tuncertain significance
rs299532610:135,097,434A/Gbenign
rs20217382110:135,097,449T/Clikely benign
rs75202528910:135,097,505A/Guncertain significance
rs158982222710:135,097,508T/Cpathogenic
rs75096275210:135,098,596C/Tuncertain significance
rs13872529010:135,098,611G/Alikely benign
rs249360559410:135,098,613T/Cuncertain significance
rs300833410:135,098,672G/Abenign
rs36910468910:135,098,726G/Alikely benign
rs37755824110:135,098,753C/Tlikely benign
rs20064787510:135,098,943G/Alikely benign
rs129748286110:135,098,963T/Cuncertain significance
rs124824663310:135,098,971G/Alikely benign
rs144999924710:135,099,012C/Gconflicting classifications of pathogenicity
rs37488340310:135,099,021C/Tuncertain significance
rs14222878010:135,099,030C/Tlikely benign
rs14854699610:135,099,038G/Auncertain significance
rs15113245610:135,099,053G/Alikely benign
rs117580375610:135,101,636G/Auncertain significance
rs37319775910:135,101,714C/Tlikely benign
rs249361544910:135,101,766T/Cuncertain significance
rs77691338810:135,101,803G/Auncertain significance
rs249361560710:135,101,815T/Cuncertain significance
rs14209418910:135,102,367C/Guncertain significance
rs249361782110:135,102,503C/Guncertain significance
rs143957694110:135,102,517A/Glikely benign
rs14296998910:135,102,561T/Cintron variant
rs14838865310:135,103,353T/Clikely benign
rs14194597910:135,103,416G/Alikely benign
rs249362105010:135,103,418T/Cuncertain significance
rs76977322510:135,103,445G/Auncertain significance
rs14565767810:135,103,451C/Tconflicting classifications of pathogenicity
rs249362126710:135,103,468A/Guncertain significance
rs145754160710:135,103,474C/Guncertain significance
rs11303523410:135,104,827C/Tlikely benign
rs499373510:135,105,966G/Abenign
rs286476810:135,105,983C/Tbenign
rs7286479310:135,105,991G/Abenign
rs20131080910:135,105,996G/Alikely benign
rs13829682610:135,106,008T/Clikely benign
rs7651186810:135,106,014G/Alikely benign
rs15055329310:135,106,039T/Cuncertain significance
rs77485384310:135,106,070C/Tuncertain significance
rs19991009110:135,106,072G/Aconflicting classifications of pathogenicity
rs14460847410:135,106,102G/Auncertain significance
rs11279532210:135,106,137G/Alikely benign
rs14756753710:135,106,173G/Alikely benign
rs36878555910:135,106,181C/Tuncertain significance
rs56712064410:135,106,184C/Tuncertain significance
rs37506103110:135,106,533G/Alikely benign
rs20032038210:135,106,539G/Alikely benign
rs15107726910:135,106,544G/Alikely benign
rs14104212210:135,106,550G/Alikely benign
rs3483247710:135,106,570G/Auncertain significance
rs14073340310:135,106,607C/Tlikely benign
rs20156711510:135,106,608G/Auncertain significance
rs249363787010:135,106,636C/Tpathogenic
rs20012933810:135,106,678G/Aconflicting classifications of pathogenicity
rs14562426810:135,106,685G/Alikely benign
rs13823077310:135,106,689G/Auncertain significance
rs184740576810:135,106,710C/Tuncertain significance
rs15013127110:135,106,712G/Alikely benign
rs56419043710:135,106,719A/Cuncertain significance
rs11138751110:135,106,733T/Clikely benign
rs136007440210:135,107,065C/Guncertain significance
rs76693900910:135,107,077G/Alikely benign
rs76001549710:135,107,082A/Tuncertain significance
rs14833774110:135,107,088C/Tuncertain significance
rs117430828810:135,107,120C/Tuncertain significance
rs26760242310:135,107,131G/Cuncertain significance
rs75605687910:135,107,160G/Auncertain significance

Showing 100 of 129 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.