UBA5

ubiquitin like modifier activating enzyme 5

Summary

This gene encodes a member of the E1-like ubiquitin-activating enzyme family. This protein activates ubiquitin-fold modifier 1, a ubiquitin-like post-translational modifier protein, via the formation of a high-energy thioester bond. Alternative splicing results in multiple transcript variants. A pseudogene of this gene has been identified on chromosome 1. [provided by RefSeq, Feb 2016]

Known Variants205 total

rsidPosition (GRCh37)AllelesClassClinVar
rs1510488993:132,378,559C/Aconflicting classifications of pathogenicity
rs7807649783:132,379,348C/Tlikely benign
rs5347092703:132,379,373G/Alikely benign
rs21079219413:132,379,382A/Gpathogenic
rs14345322393:132,379,385G/Auncertain significance
rs8984678883:132,379,386C/Tuncertain significance
rs12445591913:132,379,387G/Alikely benign
rs12953685643:132,379,391T/Cuncertain significance
rs7707496043:132,379,401G/Alikely benign
rs3768910803:132,379,402C/Tlikely benign
rs7627940753:132,379,421G/Auncertain significance
rs5744105893:132,379,444G/Alikely benign
rs14092550693:132,379,457C/Guncertain significance
rs14442090363:132,379,465G/Alikely benign
rs21079222583:132,379,472G/Tuncertain significance
rs3724706183:132,379,488G/Auncertain significance
rs11830946453:132,379,491G/Auncertain significance
rs7556960453:132,379,496C/Tuncertain significance
rs14082984683:132,379,512G/Cuncertain significance
rs1411016233:132,379,516A/Glikely benign
rs3760426253:132,379,554C/Alikely benign
rs7816058973:132,379,557C/Glikely benign
rs9096333193:132,379,558G/Clikely benign
rs7460573413:132,379,561C/Tlikely benign
rs1495168563:132,379,880T/Alikely benign
rs11982879873:132,379,900T/Clikely benign
rs789102113:132,382,722G/A
rs25303028513:132,384,649A/Glikely benign
rs7461750513:132,384,650T/Clikely benign
rs15599890063:132,384,652T/Clikely benign
rs7699198373:132,384,660T/Cconflicting classifications of pathogenicity
rs7686871333:132,384,668C/Tuncertain significance
rs7743186113:132,384,669G/Amissense variantpathogenic
rs5321787913:132,384,674A/Gmissense variantpathogenic
rs8860397563:132,384,686C/Tstop gainedpathogenic
rs1467188473:132,384,700A/Glikely benign
rs617481063:132,384,704G/Tlikely pathogenic
rs25303030073:132,384,708A/Cuncertain significance
rs13632487103:132,384,709T/Glikely pathogenic
rs7591571553:132,384,718A/Cuncertain significance
rs9889720193:132,384,811T/Clikely benign
rs7789570973:132,384,834C/Tconflicting classifications of pathogenicity
rs1503132603:132,384,835G/Aconflicting classifications of pathogenicity
rs12187407883:132,384,839C/Tlikely benign
rs21079321003:132,384,840T/Guncertain significance
rs7731554303:132,384,845C/Tlikely benign
rs7468156123:132,384,846G/Auncertain significance
rs7592505243:132,384,857A/Glikely benign
rs7751517313:132,384,894C/Tlikely benign
rs7625027673:132,384,896G/Clikely benign
rs7679399633:132,384,897A/Guncertain significance
rs25303039603:132,384,900A/Glikely pathogenic
rs7650759233:132,384,910T/Cuncertain significance
rs25303040113:132,384,919T/Clikely pathogenic
rs25303150163:132,387,647C/Alikely benign
rs7625883463:132,387,692C/Tlikely benign
rs14079453403:132,387,693T/Cuncertain significance
rs14444459943:132,387,706T/Guncertain significance
rs21079372233:132,387,745A/Glikely benign
rs3742317413:132,387,754A/Clikely benign
rs21079372923:132,387,772G/Tlikely pathogenic
rs7654756093:132,387,786A/Tlikely benign
rs21079397603:132,389,030T/Clikely benign
rs21079397683:132,389,038T/Alikely benign
rs25303213203:132,389,053C/Guncertain significance
rs19385441573:132,389,054T/Clikely benign
rs13708753103:132,389,065T/Guncertain significance
rs2007646673:132,389,069A/Glikely benign
rs13582183033:132,389,074A/Guncertain significance
rs3762470713:132,389,080A/Guncertain significance
rs7611695623:132,389,094G/Auncertain significance
rs25303216133:132,389,096G/Alikely benign
rs13662149993:132,389,116T/Cuncertain significance
rs1831768463:132,389,146G/Tlikely benign
rs3703539163:132,389,791C/Tlikely benign
rs7715410903:132,389,794A/Glikely benign
rs7771722953:132,389,795T/Clikely benign
rs13421242453:132,389,815T/Clikely benign
rs8860397613:132,389,817G/Amissense variantpathogenic
rs19385751923:132,389,819T/Clikely benign
rs7814811373:132,389,824A/Cuncertain significance
rs7631733063:132,389,826A/Guncertain significance
rs21079412613:132,389,829G/Auncertain significance
rs19385760563:132,389,839T/Clikely benign
rs25303256603:132,389,856G/Alikely pathogenic
rs14763813183:132,389,864A/Guncertain significance
rs7504525343:132,389,865A/Guncertain significance
rs3740523333:132,389,876C/Tstop gainedpathogenic
rs3681033113:132,389,877G/Tuncertain significance
rs14755444533:132,389,878A/Clikely benign
rs25303257783:132,389,881G/Auncertain significance
rs19385792873:132,389,889A/Guncertain significance
rs1879337873:132,389,912C/Tlikely benign
rs10504514083:132,390,606C/Tlikely benign
rs3684092953:132,390,609A/Glikely benign
rs8878873393:132,390,615A/Clikely benign
rs10063801653:132,390,622C/Tuncertain significance
rs25303301213:132,390,644A/Glikely benign
rs19386183263:132,390,664G/Cuncertain significance
rs25303302403:132,390,665T/Clikely benign

Showing 100 of 205 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.