UBE2H

ubiquitin conjugating enzyme E2 H

Summary

The modification of proteins with ubiquitin is an important cellular mechanism for targeting abnormal or short-lived proteins for degradation. Ubiquitination involves at least three classes of enzymes: ubiquitin-activating enzymes, or E1s, ubiquitin-conjugating enzymes, or E2s, and ubiquitin-protein ligases, or E3s. This gene encodes a member of the E2 ubiquitin-conjugating enzyme family. The encoded protein sequence is 100% identical to the mouse homolog and 98% identical to the frog and zebrafish homologs. Three alternatively spliced transcript variants have been found for this gene and they encode distinct isoforms. [provided by RefSeq, Feb 2011]

Known Variants13 total

rsidPosition (GRCh37)AllelesClassClinVar
rs12536239897:129,474,850C/Auncertain significance
rs5296705447:129,474,870C/Tlikely benign
rs3758845387:129,474,885G/Alikely benign
rs125398007:129,479,138T/Csynonymous variantbenign
rs7772570137:129,497,412G/Alikely benign
rs3744564477:129,507,624A/T
rs15544342167:129,519,477A/Guncertain significance
rs175593017:129,531,693T/Cintron variant
rs563231177:129,546,052C/Tintron variant
rs624915337:129,564,134T/Cintron variant
rs624893767:129,583,934T/Cintron variant
rs801158107:129,584,604G/Aregulatory region variant
rs803499607:129,589,868T/Cregulatory region variant

Gene information from NCBI Gene. Variant classifications from ClinVar.