UBE4A

ubiquitination factor E4A

Summary

This gene encodes a member of the U-box ubiquitin ligase family. The encoded protein is involved in multiubiquitin chain assembly and plays a critical role in chromosome condensation and separation through the polyubiquitination of securin. Autoantibodies against the encoded protein may be markers for scleroderma and Crohn's disease. A pseudogene of this gene is located on the long arm of chromosome 3. Alternatively spliced transcript variants encoding multiple isoforms have been observed for this gene. [provided by RefSeq, Feb 2011]

Known Variants55 total

rsidPosition (GRCh37)AllelesClassClinVar
rs77725500111:118,235,805C/Auncertain significance
rs77088771311:118,239,384G/Auncertain significance
rs249694372511:118,239,441C/Tlikely pathogenic
rs54954862011:118,239,847C/G
rs20106979511:118,240,151G/Cuncertain significance
rs7361394011:118,240,160G/Clikely benign
rs57462131011:118,240,177G/Auncertain significance
rs213408930511:118,240,226G/Apathogenic
rs50251411:118,241,995T/Cintron variant
rs77888315411:118,242,296C/Tuncertain significance
rs7361394611:118,242,339T/Alikely benign
rs249695306611:118,243,286A/Guncertain significance
rs74892697611:118,243,291C/Tpathogenic
rs77471125011:118,243,300C/Tuncertain significance
rs37604001611:118,243,374G/Cuncertain significance
rs14987137411:118,243,401C/Glikely benign
rs122537641611:118,243,818G/Cuncertain significance
rs14439634911:118,243,912G/Cuncertain significance
rs132640986411:118,243,965A/Guncertain significance
rs75374765311:118,243,968C/Auncertain significance
rs36792330611:118,243,997G/Auncertain significance
rs249695606011:118,244,290A/Guncertain significance
rs125202858811:118,244,356T/Auncertain significance
rs6190092911:118,245,440C/Tintron variant
rs249695957511:118,245,665C/Guncertain significance
rs78247613011:118,245,677A/Tuncertain significance
rs78204996211:118,245,717A/Tuncertain significance
rs134782811911:118,245,719G/Auncertain significance
rs147588959611:118,245,778G/Auncertain significance
rs249696008311:118,245,785T/Guncertain significance
rs249696031311:118,245,842T/Auncertain significance
rs155512518811:118,245,912A/Guncertain significance
rs14533683211:118,245,918G/Auncertain significance
rs249696063411:118,245,930A/Guncertain significance
rs7813450611:118,248,987G/A
rs78191687211:118,250,167T/Auncertain significance
rs54464959811:118,250,246G/Tuncertain significance
rs78235486311:118,250,255A/Guncertain significance
rs78237359011:118,250,261C/Tuncertain significance
rs14563000411:118,250,262G/Auncertain significance
rs14357303711:118,250,371A/Glikely benign
rs13792826411:118,250,436A/Guncertain significance
rs143371081111:118,252,147C/Tuncertain significance
rs155512649711:118,253,313T/Auncertain significance
rs249698161511:118,253,366T/Cuncertain significance
rs15069182011:118,253,408G/Auncertain significance
rs140758645711:118,253,414G/Auncertain significance
rs78180951711:118,253,479A/Guncertain significance
rs78217460511:118,255,570G/Cuncertain significance
rs14010410011:118,257,193G/Auncertain significance
rs249700729111:118,261,389G/Auncertain significance
rs36900491511:118,261,437C/Tuncertain significance
rs14229929411:118,261,438A/Gbenign
rs78204864111:118,263,525A/Tuncertain significance
rs155512972711:118,267,111C/Tuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.