UBE4B

ubiquitination factor E4B

Summary

The modification of proteins with ubiquitin is an important cellular mechanism for targeting abnormal or short-lived proteins for degradation. Ubiquitination involves at least three classes of enzymes: ubiquitin-activating enzymes, or E1s, ubiquitin-conjugating enzymes, or E2s, and ubiquitin-protein ligases, or E3s. This gene encodes an additional conjugation factor, E4, which is involved in multiubiquitin chain assembly. This gene is also the strongest candidate in the neuroblastoma tumor suppressor genes. Alternatively spliced transcript variants encoding distinct isoforms have been found for this gene. [provided by RefSeq, Jul 2008]

Known Variants68 total

rsidPosition (GRCh37)AllelesClassClinVar
rs15707486371:10,093,761G/Tlikely benign
rs1870313321:10,113,828G/Adownstream gene variant
rs12186902501:10,132,153C/Tuncertain significance
rs5754823881:10,132,203G/Auncertain significance
rs7572746121:10,132,241G/Auncertain significance
rs43338511:10,146,179G/Aintron variant
rs1471386531:10,155,522T/Guncertain significance
rs7758887711:10,155,567G/Cuncertain significance
rs785196711:10,161,163A/Cbenign
rs412807901:10,161,264G/Alikely benign
rs1892625531:10,161,265A/Glikely benign
rs13964750921:10,163,038G/Cuncertain significance
rs1465444331:10,163,148A/Guncertain significance
rs7653675881:10,165,580C/Guncertain significance
rs7520099161:10,165,612A/Tuncertain significance
rs3705261931:10,165,627A/Tuncertain significance
rs8670518861:10,165,628T/Cuncertain significance
rs13661699961:10,165,784G/Tuncertain significance
rs1996438421:10,166,317C/Tuncertain significance
rs7721531101:10,166,338G/Auncertain significance
rs25227429831:10,166,376A/Guncertain significance
rs7552921651:10,166,428C/Tuncertain significance
rs2017368321:10,166,467C/Tuncertain significance
rs9792601681:10,166,496C/Tuncertain significance
rs7559961531:10,166,502C/Auncertain significance
rs7693313641:10,166,505C/Guncertain significance
rs5715422061:10,166,517A/Guncertain significance
rs5393675511:10,166,556A/Tuncertain significance
rs7804562511:10,166,605C/Tuncertain significance
rs3747997481:10,166,625C/Guncertain significance
rs1875855301:10,167,425G/Aintron variant
rs16453318361:10,177,577A/Tuncertain significance
rs25228118321:10,177,581T/Cuncertain significance
rs1435115791:10,177,642A/Guncertain significance
rs9838771671:10,177,656A/Guncertain significance
rs1454261871:10,179,562C/Tbenign
rs781184111:10,179,615C/Tbenign
rs3763490161:10,186,910G/Cuncertain significance
rs11883524321:10,186,928C/Tuncertain significance
rs7521245011:10,189,457G/Auncertain significance
rs25228963701:10,190,826T/Clikely benign
rs16455806561:10,190,861A/Cuncertain significance
rs1507742691:10,195,079A/Guncertain significance
rs3708760931:10,195,146C/Tuncertain significance
rs1380563711:10,195,185A/Gbenign
rs7803304551:10,195,197G/Auncertain significance
rs7596616091:10,197,217T/Guncertain significance
rs7557005471:10,197,242G/Auncertain significance
rs7772817431:10,209,274A/Guncertain significance
rs2012228001:10,211,395A/Cuncertain significance
rs11915344891:10,211,439G/Cuncertain significance
rs9751971521:10,212,091C/T
rs617829371:10,223,618T/Cdownstream gene variant
rs1479611711:10,228,220G/Cbenign
rs7534347061:10,228,243C/Guncertain significance
rs25231194091:10,228,302C/Tuncertain significance
rs111215251:10,234,529C/Tintron variant
rs75404311:10,235,512G/T
rs7625005081:10,238,798G/Auncertain significance
rs1439090661:10,238,832C/Tuncertain significance
rs7573532021:10,238,837G/Auncertain significance
rs7565595911:10,238,846G/Auncertain significance
rs25231787971:10,239,476C/Tuncertain significance
rs12888406331:10,239,502C/Auncertain significance
rs12644820271:10,239,510G/Auncertain significance
rs1466864751:10,239,569C/Guncertain significance
rs1391089391:10,239,586C/Tbenign
rs25231793421:10,239,587C/Tuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.