UBXN6

UBX domain protein 6

Summary

Enables ATPase binding activity. Involved in ERAD pathway; endosome to lysosome transport via multivesicular body sorting pathway; and macroautophagy. Located in bounding membrane of organelle and cytosol. Part of endosome and protein-containing complex. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants45 total

rsidPosition (GRCh37)AllelesClassClinVar
rs13812903619:4,445,527C/Tuncertain significance
rs134564997919:4,445,549C/Guncertain significance
rs74946287719:4,445,551C/Tuncertain significance
rs7707757319:4,445,559G/Auncertain significance
rs20055589019:4,445,581C/Tuncertain significance
rs53808610619:4,445,584C/Tuncertain significance
rs77571360219:4,446,156C/Auncertain significance
rs20132218219:4,446,358T/Cuncertain significance
rs78121964919:4,446,378C/Tuncertain significance
rs75631307819:4,446,381A/Guncertain significance
rs37553359019:4,446,385C/Guncertain significance
rs20151766619:4,446,393C/Auncertain significance
rs77626894419:4,446,394G/Auncertain significance
rs53292976819:4,446,536T/Cuncertain significance
rs76524839319:4,446,538G/Tuncertain significance
rs14760666819:4,446,564G/Tuncertain significance
rs15106005719:4,446,615C/Tuncertain significance
rs20139492619:4,446,618G/Auncertain significance
rs810196119:4,446,629G/Auncertain significance
rs119999928619:4,446,648T/Cuncertain significance
rs20089870119:4,446,680G/Cuncertain significance
rs20062989319:4,446,683G/Cuncertain significance
rs13834261319:4,446,871A/Guncertain significance
rs14961034719:4,446,888G/Alikely benign
rs75898430119:4,446,914G/Auncertain significance
rs251233770719:4,446,916T/Cuncertain significance
rs36778682919:4,447,588C/Tuncertain significance
rs14139150219:4,447,594C/Tuncertain significance
rs37618263619:4,447,598G/Tuncertain significance
rs214517339919:4,447,603G/Cuncertain significance
rs75604242119:4,448,366G/Auncertain significance
rs20077596219:4,452,441C/Tuncertain significance
rs76593486719:4,452,482T/Cuncertain significance
rs41183319:4,453,325G/Cdownstream gene variant
rs115822594919:4,453,462G/Cuncertain significance
rs76452592619:4,453,484C/Tuncertain significance
rs116474738819:4,453,508G/Auncertain significance
rs53392791219:4,453,950G/Auncertain significance
rs20029173019:4,453,969G/Auncertain significance
rs197470059519:4,454,002C/Tuncertain significance
rs57654456119:4,454,040C/Tuncertain significance
rs78059597719:4,454,055G/Auncertain significance
rs112788819:4,454,083C/Tmissense variant
rs74744959819:4,457,637C/Tuncertain significance
rs18335673219:4,458,656G/Acoding sequence variant

Gene information from NCBI Gene. Variant classifications from ClinVar.