UHRF2

ubiquitin like with PHD and ring finger domains 2

Summary

This gene encodes a nuclear protein which is involved in cell-cycle regulation. The encoded protein is a ubiquitin-ligase capable of ubiquinating PCNP (PEST-containing nuclear protein), and together they may play a role in tumorigenesis. The encoded protein contains an NIRF_N domain, a PHD finger, a set- and ring-associated (SRA) domain, and a RING finger domain and several of these domains have been shown to be essential for the regulation of cell proliferation. This protein may also have a role in intranuclear degradation of polyglutamine aggregates. Alternative splicing results in multiple transcript variants some of which are non-protein coding. [provided by RefSeq, Feb 2012]

Known Variants36 total

rsidPosition (GRCh37)AllelesClassClinVar
rs7534591049:6,413,540A/Guncertain significance
rs24886822589:6,413,602G/Tuncertain significance
rs107587869:6,418,822C/A
rs3766066739:6,421,013A/Glikely benign
rs5576008379:6,421,036C/Guncertain significance
rs24887052909:6,421,072T/Cuncertain significance
rs12564789189:6,421,096C/Tuncertain significance
rs7489660339:6,421,104C/Tuncertain significance
rs1500946309:6,421,117T/Cuncertain significance
rs3732517409:6,421,135T/Cuncertain significance
rs132836629:6,428,530T/C
rs5558918739:6,432,164C/T
rs24887475459:6,433,989G/Tuncertain significance
rs24887477759:6,434,038C/Auncertain significance
rs24887480079:6,434,080A/Guncertain significance
rs1427725339:6,434,088A/Cuncertain significance
rs3717808919:6,434,148G/Auncertain significance
rs5718985879:6,438,753A/G
rs4141079:6,439,294C/Tintron variant
rs1115209349:6,446,119A/Gintron variant
rs12191941519:6,460,714C/Guncertain significance
rs12985540539:6,460,772C/Tuncertain significance
rs132836879:6,473,296A/Gupstream gene variant
rs9796600659:6,477,625G/Auncertain significance
rs24888888089:6,477,750G/Tuncertain significance
rs7731329919:6,477,754A/Tuncertain significance
rs7695952529:6,481,750G/Auncertain significance
rs169246319:6,486,308G/Cintron variant
rs7769600279:6,499,902G/Cuncertain significance
rs7727513739:6,500,575G/Tuncertain significance
rs2016016749:6,500,594C/Tuncertain significance
rs24889683159:6,500,686C/Guncertain significance
rs733942999:6,502,429T/G
rs7676657769:6,504,608T/Auncertain significance
rs13294721149:6,504,675T/Guncertain significance
rs7586212719:6,506,127T/Auncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.