UPB1

beta-ureidopropionase 1

Summary

This gene encodes a protein that belongs to the CN hydrolase family. Beta-ureidopropionase catalyzes the last step in the pyrimidine degradation pathway. The pyrimidine bases uracil and thymine are degraded via the consecutive action of dihydropyrimidine dehydrogenase (DHPDH), dihydropyrimidinase (DHP) and beta-ureidopropionase (UP) to beta-alanine and beta-aminoisobutyric acid, respectively. UP deficiencies are associated with N-carbamyl-beta-amino aciduria and may lead to abnormalities in neurological activity. [provided by RefSeq, Jul 2008]

Known Variants177 total

rsidPosition (GRCh37)AllelesClassClinVar
rs207047422:24,891,292G/Cbenign
rs57470097222:24,891,293C/Tuncertain significance
rs88605728822:24,891,307T/Cuncertain significance
rs11662968722:24,891,309C/Tlikely benign
rs57581195722:24,891,311C/Tuncertain significance
rs78031413122:24,891,345G/Cuncertain significance
rs207047522:24,891,355A/Tbenign
rs54116995222:24,891,361G/Auncertain significance
rs20067738722:24,891,365C/Glikely benign
rs76493223222:24,891,376C/Guncertain significance
rs20155902922:24,891,380C/Tlikely benign
rs37126259122:24,891,381G/Auncertain significance
rs204384863422:24,891,396C/Tlikely benign
rs75510439422:24,891,397T/Cuncertain significance
rs20068854622:24,891,409T/Cconflicting classifications of pathogenicity
rs76473746622:24,891,412A/Guncertain significance
rs19993420722:24,891,418A/Clikely benign
rs18571977422:24,891,425G/Aconflicting classifications of pathogenicity
rs37586382122:24,891,430C/Tuncertain significance
rs14892676122:24,891,433A/Tuncertain significance
rs14189692922:24,891,453G/Alikely benign
rs20014579722:24,891,462G/Aconflicting classifications of pathogenicity
rs14585694822:24,893,867G/Aupstream gene variant
rs223286522:24,896,014A/Gnot provided
rs18425776322:24,896,069A/Glikely benign
rs13808180022:24,896,073A/Gsplice region variantpathogenic
rs78048413422:24,896,087G/Alikely benign
rs74761535622:24,896,097G/Auncertain significance
rs74685512522:24,896,103G/Auncertain significance
rs37357351222:24,896,112T/Cuncertain significance
rs14598949822:24,896,113C/Guncertain significance
rs37367340322:24,896,155C/Tuncertain significance
rs14822576722:24,896,161A/Guncertain significance
rs75627220022:24,896,163C/Tpathogenic
rs76614853422:24,896,173G/Auncertain significance
rs75411535522:24,896,176C/Tuncertain significance
rs75553317022:24,896,178C/Tuncertain significance
rs12190806622:24,896,179G/Amissense variantuncertain significance
rs37771391222:24,896,189C/Tlikely benign
rs15074048822:24,896,195G/Tconflicting classifications of pathogenicity
rs94461097522:24,896,222C/Tlikely benign
rs56581039922:24,896,223G/Auncertain significance
rs3403508522:24,896,224C/Tmissense variantuncertain significance
rs75890489922:24,896,245A/Guncertain significance
rs251796133822:24,896,266T/Clikely benign
rs14322059922:24,896,409C/Gregulatory region variant
rs75671900322:24,898,108T/Clikely benign
rs75005755422:24,898,113G/Auncertain significance
rs77985916622:24,898,120G/Cuncertain significance
rs77879382822:24,898,126C/Tlikely benign
rs117640211522:24,898,127G/Aconflicting classifications of pathogenicity
rs204400529822:24,898,142A/Guncertain significance
rs14015711322:24,898,169C/Tpathogenic
rs77009139422:24,898,171G/Aconflicting classifications of pathogenicity
rs13887200122:24,898,175G/Tconflicting classifications of pathogenicity
rs101934508022:24,898,182G/Clikely pathogenic
rs77221250222:24,898,187T/Gpathogenic
rs14743963722:24,898,369T/Glikely benign
rs18125177822:24,901,968A/Gintron variant
rs7957140022:24,906,650G/Anot provided
rs75266706722:24,906,698C/Tlikely benign
rs37076004522:24,906,709A/Glikely benign
rs20016128122:24,906,736T/Cconflicting classifications of pathogenicity
rs14536879822:24,906,738C/Guncertain significance
rs14918776022:24,906,739G/Aconflicting classifications of pathogenicity
rs149054710922:24,906,750T/Guncertain significance
rs77567659822:24,906,751T/Glikely benign
rs76204575722:24,909,279A/Glikely benign
rs19978863222:24,909,296C/Tconflicting classifications of pathogenicity
rs76697038922:24,909,297G/Alikely benign
rs214702601222:24,909,304C/Tuncertain significance
rs204423962222:24,909,320T/Cuncertain significance
rs77064403622:24,909,337C/Tlikely pathogenic
rs37235741522:24,909,338G/Auncertain significance
rs156898980522:24,909,341A/Guncertain significance
rs14574983622:24,909,346G/Aconflicting classifications of pathogenicity
rs37186603922:24,909,371C/Tuncertain significance
rs77329627722:24,909,375C/Tlikely benign
rs76089635122:24,909,383T/Auncertain significance
rs77709970422:24,909,394G/Auncertain significance
rs14485948222:24,909,405G/Alikely benign
rs138494142122:24,911,187G/Auncertain significance
rs14929460722:24,911,204C/Tlikely benign
rs14352122022:24,911,205G/Auncertain significance
rs14799442622:24,911,216G/Alikely benign
rs129603449222:24,911,217C/Tpathogenic
rs14343814022:24,911,222C/Guncertain significance
rs14713352322:24,911,223G/Auncertain significance
rs77377455022:24,911,231C/Tconflicting classifications of pathogenicity
rs204427303022:24,911,237G/Auncertain significance
rs7488316522:24,911,249C/Tbenign
rs76619601122:24,911,250G/Auncertain significance
rs75492390522:24,911,254G/Auncertain significance
rs160150524222:24,911,278T/Auncertain significance
rs15069082922:24,911,279G/Auncertain significance
rs89882030522:24,911,291C/Tlikely benign
rs104738934622:24,911,301A/Guncertain significance
rs36868841422:24,911,304A/Guncertain significance
rs75363883722:24,911,317C/Tconflicting classifications of pathogenicity
rs20050819022:24,911,318G/Alikely benign

Showing 100 of 177 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.