USP15

ubiquitin specific peptidase 15

Summary

This gene encodes a member of the ubiquitin specific protease (USP) family of deubiquitinating enzymes. USP enzymes play critical roles in ubiquitin-dependent processes through polyubiquitin chain disassembly and hydrolysis of ubiquitin-substrate bonds. The encoded protein associates with the COP9 signalosome, and also plays a role in transforming growth factor beta signalling through deubiquitination of receptor-activated SMAD transcription factors. Alternatively spliced transcript variants encoding multiple isoforms have been observed for this gene, and a pseudogene of this gene is located on the long arm of chromosome 2. [provided by RefSeq, Nov 2011]

Known Variants40 total

rsidPosition (GRCh37)AllelesClassClinVar
rs5611781012:62,656,247A/Gupstream gene variant
rs107495812:62,664,272C/Tintron variant
rs797506512:62,680,603G/Aintron variant
rs76650281312:62,688,057G/Auncertain significance
rs1117442012:62,696,599C/Tbenign
rs254118812512:62,715,268A/Guncertain significance
rs76840727312:62,719,682T/Auncertain significance
rs206510934012:62,719,704T/Cuncertain significance
rs7313752112:62,720,287T/Cintron variant
rs54617311112:62,726,596A/C
rs74871447512:62,749,142A/Glikely benign
rs14038067412:62,749,194C/Guncertain significance
rs1281436912:62,766,966A/C
rs797002812:62,774,082C/Tintron variant
rs75336034412:62,775,424G/Auncertain significance
rs5629875612:62,777,565G/Tintron variant
rs95253626012:62,777,624C/Guncertain significance
rs254064046912:62,777,901G/Tuncertain significance
rs13916627112:62,777,920T/Cuncertain significance
rs3601107712:62,777,981A/Glikely benign
rs204484612:62,778,065A/Gbenign
rs120609899912:62,783,243A/Guncertain significance
rs91093195412:62,783,249T/Auncertain significance
rs94939172812:62,783,389T/Cuncertain significance
rs74667540212:62,783,399T/Clikely benign
rs37030593012:62,783,429C/Tlikely benign
rs122966411912:62,783,617G/Auncertain significance
rs75391321412:62,784,651G/Auncertain significance
rs20203754112:62,784,700G/Tuncertain significance
rs254066068312:62,784,721G/Auncertain significance
rs124362197812:62,784,738A/Tuncertain significance
rs254066174312:62,784,990C/Guncertain significance
rs13916185612:62,785,037T/Guncertain significance
rs1117445712:62,785,663C/Tbenign
rs77191457212:62,786,858C/Guncertain significance
rs254066783412:62,786,909G/Auncertain significance
rs37461235212:62,790,124C/Auncertain significance
rs75779743212:62,798,106A/Guncertain significance
rs143856506412:62,798,111A/Guncertain significance
rs254069680112:62,798,142T/Guncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.