VMA12

vacuolar ATPase assembly factor VMA12

Summary

The protein encoded by this gene has been observed to localize to the endoplasmic reticulum (ER)-Golgi intermediate compartment (ERGIC) and coat protein complex I (COPI) in some human cells. The encoded protein shares some homology with the yeast protein Vma12. Defects in this gene are a cause of congenital disorder of glycosylation, type IIp. [provided by RefSeq, Mar 2016]

Known Variants59 total

rsidPosition (GRCh37)AllelesClassClinVar
rs1155597817:26,684,368G/Alikely benign
rs479542917:26,684,449G/Cbenign
rs14728313717:26,684,709C/Tuncertain significance
rs78267110217:26,684,712G/Auncertain significance
rs78193958017:26,684,729G/Aconflicting classifications of pathogenicity
rs14831941117:26,684,737T/Cbenign
rs37377501817:26,684,767G/Tuncertain significance
rs78224420017:26,684,793C/Tuncertain significance
rs14143290317:26,684,803C/Tuncertain significance
rs18190270817:26,684,831T/Clikely benign
rs140544666517:26,684,836C/Guncertain significance
rs78211973917:26,684,844C/Tuncertain significance
rs11691444217:26,684,849A/Glikely benign
rs78264365017:26,684,868C/Tuncertain significance
rs78182368417:26,684,870C/Tlikely benign
rs13923935217:26,684,905G/Alikely pathogenic
rs37388563017:26,684,914A/Clikely benign
rs78276758117:26,684,920C/Tlikely benign
rs78243019617:26,685,942C/Tuncertain significance
rs36764562017:26,685,957A/Guncertain significance
rs3527601217:26,685,983T/Clikely benign
rs20061611717:26,685,995G/Auncertain significance
rs20197501517:26,686,011G/Auncertain significance
rs78242847717:26,686,387A/Guncertain significance
rs78234405917:26,686,394A/Cuncertain significance
rs14496062417:26,686,401C/Tuncertain significance
rs78204631317:26,686,402G/Auncertain significance
rs1153892717:26,686,416G/Abenign
rs155558173717:26,686,435C/Tlikely benign
rs1780273617:26,686,445G/Abenign
rs1696422617:26,686,552G/Alikely benign
rs18487803717:26,687,533T/Abenign
rs155558190817:26,687,535C/Tlikely benign
rs190829060117:26,687,542T/Clikely benign
rs103683220417:26,687,552G/Cuncertain significance
rs78230418317:26,687,590G/Alikely benign
rs37584823617:26,687,747C/Tbenign
rs78279208117:26,687,752C/Glikely benign
rs37757910717:26,687,767T/Cuncertain significance
rs18809655417:26,687,789C/Tlikely benign
rs138694521517:26,687,794A/Guncertain significance
rs250813115517:26,687,806C/Tuncertain significance
rs1257217:26,687,811G/Abenign
rs3610614717:26,687,835C/Gbenign
rs250813159117:26,687,865G/Tuncertain significance
rs128634097717:26,687,866C/Tuncertain significance
rs20037752217:26,687,869C/Tuncertain significance
rs7718704817:26,688,065C/Tlikely benign
rs14711657817:26,688,179C/Tuncertain significance
rs78253840717:26,688,187A/Glikely benign
rs78266679317:26,688,189C/Guncertain significance
rs76116701617:26,688,194T/Clikely benign
rs148132147917:26,688,216G/Auncertain significance
rs78200217517:26,688,224G/Auncertain significance
rs54952006117:26,688,233G/Auncertain significance
rs155558212417:26,688,239G/Tuncertain significance
rs78206632017:26,688,242C/Guncertain significance
rs14774279717:26,688,243G/Auncertain significance
rs14829214517:26,688,481T/Clikely benign

Gene information from NCBI Gene. Variant classifications from ClinVar.