VNN1

vanin 1

Summary

This gene encodes a member of the vanin family of proteins, which share extensive sequence similarity with each other, and also with biotinidase. The family includes secreted and membrane-associated proteins, a few of which have been reported to participate in hematopoietic cell trafficking. No biotinidase activity has been demonstrated for any of the vanin proteins, however, they possess pantetheinase activity, which may play a role in oxidative-stress response. This protein, like its mouse homolog, is likely a GPI-anchored cell surface molecule. The mouse protein is expressed by the perivascular thymic stromal cells and regulates migration of T-cell progenitors to the thymus. This gene lies in close proximity to, and in the same transcriptional orientation as, two other vanin genes on chromosome 6q23-q24. [provided by RefSeq, Feb 2009]

Known Variants49 total

rsidPosition (GRCh37)AllelesClassClinVar
rs617295836:133,004,281A/Gbenign
rs7786574616:133,004,296A/Guncertain significance
rs3734370606:133,004,308C/Tlikely benign
rs7749751776:133,004,428G/Tuncertain significance
rs7544764216:133,004,461C/Tuncertain significance
rs9397957376:133,005,488G/Auncertain significance
rs1911631816:133,005,498A/Glikely benign
rs13496680316:133,005,500T/Guncertain significance
rs2021061286:133,005,539C/Tlikely benign
rs2010588796:133,005,614T/Clikely benign
rs359385656:133,013,432A/Gbenign
rs345350506:133,013,576G/Tbenign
rs15622156026:133,013,583T/Cuncertain significance
rs11995860506:133,013,645G/Auncertain significance
rs24833127696:133,013,649G/Auncertain significance
rs455234446:133,013,662C/Gbenign
rs7454911216:133,013,699G/Auncertain significance
rs3719349236:133,013,702T/Auncertain significance
rs454586976:133,013,726G/Abenign
rs12875473226:133,014,255A/Guncertain significance
rs7787530486:133,014,292C/Glikely benign
rs17783165126:133,014,297G/Auncertain significance
rs7578905576:133,014,306T/Cuncertain significance
rs7797303906:133,014,318A/Tuncertain significance
rs7749966926:133,014,360G/Auncertain significance
rs2007824736:133,015,133T/Cuncertain significance
rs1481271746:133,015,143C/Auncertain significance
rs1419484576:133,015,167A/Guncertain significance
rs7812682716:133,015,170C/Tuncertain significance
rs1506832156:133,015,193C/Tlikely benign
rs456243366:133,015,227C/Tbenign
rs456100326:133,015,257C/Gbenign
rs22729966:133,015,271T/Cmissense variant
rs2011698896:133,015,275T/Clikely benign
rs96899396:133,018,271T/A
rs23272756:133,024,980C/G
rs1504913496:133,025,165G/Tdownstream gene variant
rs1395984736:133,028,675A/Gintron variant
rs38230266:133,032,611G/Aintron variant
rs1473826776:133,032,854C/Tlikely benign
rs7467387776:133,032,855G/Auncertain significance
rs7809868756:133,032,863C/Guncertain significance
rs455644416:133,032,973C/Tbenign
rs7485185026:133,034,996A/Guncertain significance
rs17786364806:133,035,033C/Tuncertain significance
rs3728983706:133,035,090C/Guncertain significance
rs7659430426:133,035,150C/Tuncertain significance
rs48976126:133,035,325A/Cbenign
rs1896960806:133,036,058A/Gupstream gene variant

Gene information from NCBI Gene. Variant classifications from ClinVar.