XAB2

XPA binding protein 2

Summary

Involved in DNA-templated transcription; mRNA splicing, via spliceosome; and transcription-coupled nucleotide-excision repair. Located in nucleoplasm. Part of U2-type catalytic step 2 spliceosome. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants55 total

rsidPosition (GRCh37)AllelesClassClinVar
rs74565965819:7,684,488C/Tuncertain significance
rs251264572519:7,684,494A/Guncertain significance
rs203098185419:7,684,507G/Auncertain significance
rs77472985719:7,684,510C/Tuncertain significance
rs132749324719:7,684,651T/Cuncertain significance
rs88794539419:7,684,669C/Auncertain significance
rs74728301419:7,684,713T/Cuncertain significance
rs116394744919:7,684,728C/Tuncertain significance
rs76054766619:7,684,836C/Tuncertain significance
rs127202825219:7,684,874C/Tuncertain significance
rs77521097719:7,684,875G/Auncertain significance
rs76168399319:7,684,926C/Tuncertain significance
rs203099583919:7,684,962C/Auncertain significance
rs36940987219:7,685,169G/Auncertain significance
rs75396339019:7,685,298A/Guncertain significance
rs125647750719:7,685,311T/Guncertain significance
rs121447651419:7,685,322G/Auncertain significance
rs138370274919:7,685,462T/Cuncertain significance
rs76350710719:7,685,464T/Cuncertain significance
rs99419979419:7,685,474G/Auncertain significance
rs116884187719:7,685,542T/Auncertain significance
rs145839740919:7,685,827C/Tuncertain significance
rs37345464619:7,686,089C/Tuncertain significance
rs14125373419:7,686,090G/Auncertain significance
rs130889208819:7,686,098T/Guncertain significance
rs130521243119:7,687,258T/Cuncertain significance
rs37723322819:7,687,273C/Tuncertain significance
rs131556784119:7,687,285T/Cuncertain significance
rs37719400119:7,687,309G/Auncertain significance
rs57800143519:7,687,430G/Tuncertain significance
rs77190083719:7,687,507T/Auncertain significance
rs75319194919:7,687,526G/Auncertain significance
rs36758856319:7,687,537G/Auncertain significance
rs75682846619:7,687,540G/Auncertain significance
rs75794388319:7,687,716C/Auncertain significance
rs37022992719:7,688,667C/Tuncertain significance
rs77290326219:7,688,697T/Cuncertain significance
rs104987014719:7,688,706G/Auncertain significance
rs76324829819:7,689,210G/Cuncertain significance
rs18822628619:7,689,316C/Tuncertain significance
rs75262164519:7,690,801C/Guncertain significance
rs77909961419:7,690,810A/Cuncertain significance
rs75411767319:7,691,105G/Auncertain significance
rs413482719:7,692,060G/Adownstream gene variant
rs120631637619:7,692,174G/Cuncertain significance
rs37718082719:7,692,179A/Guncertain significance
rs77002771019:7,692,196T/Cuncertain significance
rs20104007519:7,692,211C/Tuncertain significance
rs77989742719:7,692,245C/Tuncertain significance
rs75692991319:7,692,269G/Auncertain significance
rs75539741319:7,692,670G/Auncertain significance
rs138995764719:7,693,106A/Guncertain significance
rs74993157219:7,693,124A/Cuncertain significance
rs58777783919:7,694,722G/Cmissense variantpathogenic
rs58777977919:7,696,362C/Tstop gainedpathogenic

Gene information from NCBI Gene. Variant classifications from ClinVar.