XPNPEP2

X-prolyl aminopeptidase 2

Summary

Aminopeptidase P is a hydrolase specific for N-terminal imido bonds, which are common to several collagen degradation products, neuropeptides, vasoactive peptides, and cytokines. Structurally, the enzyme is a member of the 'pita bread fold' family and occurs in mammalian tissues in both soluble and GPI-anchored membrane-bound forms. A membrane-bound and soluble form of this enzyme have been identified as products of two separate genes. [provided by RefSeq, Jul 2008]

Known Variants52 total

rsidPosition (GRCh37)AllelesClassClinVar
rs3788853X:128,870,791C/Aregulatory region variantrisk factor
rs2050011X:128,871,578G/A
rs777882575X:128,873,196C/Tlikely benign
rs5975145X:128,875,801C/Tbenign
rs5975146X:128,875,978G/Abenign
rs147873278X:128,876,155C/Guncertain significance
rs1272063889X:128,879,203G/Cuncertain significance
rs1195935972X:128,879,218A/Guncertain significance
rs1336537003X:128,880,262T/Cuncertain significance
rs1456075649X:128,880,287T/Auncertain significance
rs386352381X:128,880,312G/Auncertain significance
rs1481447777X:128,880,563T/Clikely benign
rs760111651X:128,880,585A/Guncertain significance
rs3747343X:128,880,614T/Cbenign
rs987480651X:128,880,640C/Tuncertain significance
rs2522088910X:128,881,607C/Auncertain significance
rs144619324X:128,881,635G/Tlikely benign
rs191887278X:128,881,685C/Tuncertain significance
rs138365897X:128,884,450C/Tmissense variant
rs765067524X:128,884,465T/Cuncertain significance
rs761857904X:128,884,515G/Auncertain significance
rs1316035895X:128,884,518C/Auncertain significance
rs2522096348X:128,885,729A/Cuncertain significance
rs377568487X:128,886,146G/Auncertain significance
rs2522097438X:128,886,162C/Tlikely benign
rs151254296X:128,886,229C/Tuncertain significance
rs200622189X:128,886,299G/Auncertain significance
rs192592840X:128,886,332C/Tlikely benign
rs185260305X:128,887,144G/Auncertain significance
rs1926453223X:128,887,198G/Auncertain significance
rs938361223X:128,887,206C/Glikely benign
rs145126121X:128,888,528G/Alikely benign
rs146840263X:128,888,532G/Auncertain significance
rs761953301X:128,888,554G/Auncertain significance
rs1051476258X:128,889,272A/Tuncertain significance
rs1351719626X:128,889,275A/Tuncertain significance
rs867312968X:128,889,284C/Tlikely benign
rs1220171785X:128,889,328G/Tuncertain significance
rs757139295X:128,890,513A/Cuncertain significance
rs375530554X:128,893,200C/Tuncertain significance
rs770601922X:128,894,501G/Auncertain significance
rs758120793X:128,894,545G/Auncertain significance
rs2522115614X:128,895,160A/Cuncertain significance
rs767821189X:128,895,189G/Auncertain significance
rs1926651380X:128,895,222G/Auncertain significance
rs2522117357X:128,896,002A/Cuncertain significance
rs2522126313X:128,901,600T/Guncertain significance
rs200683833X:128,901,653G/Alikely benign
rs142912864X:128,902,290C/Tlikely benign
rs144580730X:128,902,301G/Auncertain significance
rs767083060X:128,902,439C/Tuncertain significance
rs17314665X:128,902,624C/Abenign

Gene information from NCBI Gene. Variant classifications from ClinVar.