ZBTB1

zinc finger and BTB domain containing 1

Summary

Enables K63-linked polyubiquitin modification-dependent protein binding activity; protein heterodimerization activity; and protein homodimerization activity. Involved in several processes, including negative regulation of transcription by RNA polymerase II; nucleobase-containing compound biosynthetic process; and protein homooligomerization. Located in nuclear body and nuclear membrane. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants30 total

rsidPosition (GRCh37)AllelesClassClinVar
rs145300714:64,974,203A/Gregulatory region variant
rs196686514:64,975,861G/Aupstream gene variant
rs11394468414:64,976,682G/C
rs1184817914:64,977,053A/Gdownstream gene variant
rs7326774314:64,978,142G/Tregulatory region variant
rs490228814:64,982,940T/Cintron variant
rs378372414:64,983,477G/Aintron variant
rs14645622214:64,988,848C/Tuncertain significance
rs207986732014:64,988,961A/Tuncertain significance
rs19981562014:64,989,027G/Alikely benign
rs255058747514:64,989,121G/Auncertain significance
rs76398729214:64,989,162G/Auncertain significance
rs132370287314:64,989,170A/Cuncertain significance
rs1785466414:64,989,223T/Cuncertain significance
rs75099148214:64,989,255A/Guncertain significance
rs37694518414:64,989,288A/Cuncertain significance
rs13801787014:64,989,394G/Auncertain significance
rs135317014414:64,989,419A/Tuncertain significance
rs37598556314:64,989,472A/Guncertain significance
rs77663015514:64,989,494G/Cuncertain significance
rs36926524514:64,989,508C/Auncertain significance
rs156663595614:64,989,528T/Cuncertain significance
rs13919381614:64,989,673C/Auncertain significance
rs77079142714:64,989,727A/Guncertain significance
rs14297855314:64,989,728T/Guncertain significance
rs119033114814:64,989,731G/Auncertain significance
rs76724948114:64,989,732T/Guncertain significance
rs255058907314:64,989,862A/Guncertain significance
rs37236467114:64,990,206A/Guncertain significance
rs77043014714:64,990,232A/Guncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.