ZNF217

zinc finger protein 217

Summary

Enables DNA-binding transcription repressor activity, RNA polymerase II-specific and RNA polymerase II cis-regulatory region sequence-specific DNA binding activity. Involved in negative regulation of transcription by RNA polymerase II. Located in mitochondrion and nuclear speck. Part of histone deacetylase complex. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants70 total

rsidPosition (GRCh37)AllelesClassClinVar
rs105694820:52,183,705C/A
rs251570245520:52,188,348G/Tuncertain significance
rs3602967720:52,188,376T/Abenign
rs251570263320:52,188,381C/Guncertain significance
rs37052092420:52,188,389T/Cuncertain significance
rs606396520:52,191,200G/Acoding sequence variant
rs14033364420:52,192,274G/Auncertain significance
rs74741202720:52,192,289G/Auncertain significance
rs76871447220:52,192,295C/Auncertain significance
rs3449030120:52,192,297A/Glikely benign
rs37173011220:52,192,334T/Cuncertain significance
rs76692947920:52,192,362G/Auncertain significance
rs4543939520:52,192,417C/Tlikely benign
rs75627442320:52,192,435C/Tlikely benign
rs1190691320:52,192,453G/Abenign
rs20055475020:52,192,519G/Tuncertain significance
rs19964414920:52,192,534G/Alikely benign
rs74931230420:52,192,638C/Tuncertain significance
rs3573623920:52,192,648G/Cbenign
rs37107586620:52,192,667T/Cuncertain significance
rs3555636020:52,192,690G/Tbenign
rs104319874420:52,192,716G/Tuncertain significance
rs609749020:52,192,789T/Cbenign
rs76378177820:52,192,805G/Auncertain significance
rs198826797420:52,192,884C/Tuncertain significance
rs37170607120:52,192,940G/Auncertain significance
rs54962397720:52,192,958G/Auncertain significance
rs276667620:52,192,998A/Glikely benign
rs125815818620:52,193,027G/Auncertain significance
rs5626893920:52,193,032C/Tlikely benign
rs37316473620:52,193,060A/Cuncertain significance
rs37347392120:52,193,094G/Auncertain significance
rs37072450120:52,193,122C/Tuncertain significance
rs37745755820:52,193,150T/Cuncertain significance
rs75188294920:52,193,232C/Tuncertain significance
rs74699001220:52,193,300G/Auncertain significance
rs86620145020:52,193,351G/Auncertain significance
rs74578632420:52,193,523G/Tuncertain significance
rs77768370120:52,193,531A/Guncertain significance
rs6174838020:52,193,542C/Tlikely benign
rs76373287920:52,193,650A/Cuncertain significance
rs3461405220:52,193,722G/Abenign
rs251573015620:52,194,963T/Cuncertain significance
rs54999280320:52,198,135A/Guncertain significance
rs76937031820:52,198,146G/Auncertain significance
rs75299097820:52,198,158G/Auncertain significance
rs18667601720:52,198,273G/Tuncertain significance
rs77724197720:52,198,282C/Auncertain significance
rs14678256120:52,198,285C/Tuncertain significance
rs118823073820:52,198,378C/Tuncertain significance
rs13924669220:52,198,384T/Cuncertain significance
rs37007008820:52,198,419G/Auncertain significance
rs18197349520:52,198,582T/Clikely benign
rs140921632120:52,198,584G/Auncertain significance
rs91336055120:52,198,621C/Tlikely benign
rs136855083520:52,198,629G/Auncertain significance
rs251574395720:52,198,638G/Auncertain significance
rs20035039020:52,198,737C/Guncertain significance
rs36888225220:52,198,746G/Auncertain significance
rs74810437720:52,198,773G/Auncertain significance
rs75064319020:52,198,927T/Cuncertain significance
rs214595962420:52,198,942C/Guncertain significance
rs3526745120:52,198,979G/Abenign
rs96569608820:52,199,013G/Auncertain significance
rs55560971620:52,199,026G/Cuncertain significance
rs128393430520:52,199,111T/Guncertain significance
rs11272958620:52,199,264C/Tuncertain significance
rs75236172020:52,199,337G/Auncertain significance
rs276667820:52,208,356G/C
rs276667920:52,210,626A/Gregulatory region variant

Gene information from NCBI Gene. Variant classifications from ClinVar.