AADAT

aminoadipate aminotransferase

Summary

This gene encodes a protein that is highly similar to mouse and rat kynurenine aminotransferase II. The rat protein is a homodimer with two transaminase activities. One activity is the transamination of alpha-aminoadipic acid, a final step in the saccaropine pathway which is the major pathway for L-lysine catabolism. The other activity involves the transamination of kynurenine to produce kynurenine acid, the precursor of kynurenic acid which has neuroprotective properties. Several transcript variants encoding two different isoforms have been found for this gene. [provided by RefSeq, Nov 2013]

Known Variants11 total

rsidPosition (GRCh37)AllelesClassClinVar
rs24781662764:170,985,939A/Tuncertain significance
rs7548489714:170,987,628C/Guncertain significance
rs68554504:170,992,674C/Tintron variant
rs68542604:170,992,704G/Tintron variant
rs12952369194:170,994,307G/Auncertain significance
rs9636604:170,995,066C/Tintron variant
rs7766360924:170,999,723C/Auncertain significance
rs3723815274:171,009,584T/Auncertain significance
rs117327634:171,010,101G/Aintron variant
rs24783340074:171,010,777A/Tuncertain significance
rs797516624:171,014,655G/Cupstream gene variant

Gene information from NCBI Gene. Variant classifications from ClinVar.