ABCB1

ATP binding cassette subfamily B member 1

Pharmacogene

Summary

The membrane-associated protein encoded by this gene is a member of the superfamily of ATP-binding cassette (ABC) transporters. ABC proteins transport various molecules across extra- and intra-cellular membranes. ABC genes are divided into seven distinct subfamilies (ABC1, MDR/TAP, MRP, ALD, OABP, GCN20, White). This protein is a member of the MDR/TAP subfamily. Members of the MDR/TAP subfamily are involved in multidrug resistance. The protein encoded by this gene is an ATP-dependent drug efflux pump for xenobiotic compounds with broad substrate specificity. It is responsible for decreased drug accumulation in multidrug-resistant cells and often mediates the development of resistance to anticancer drugs. This protein also functions as a transporter in the blood-brain barrier. Mutations in this gene are associated with colchicine resistance and Inflammatory bowel disease 13. Alternative splicing and the use of alternative promoters results in multiple transcript variants. [provided by RefSeq, Feb 2017]

Known Variants677 total

rsidPosition (GRCh37)AllelesClassClinVar
rs15848232367:87,133,135G/Adrug response
rs15848232407:87,133,138A/Gdrug response
rs15848232447:87,133,139G/Cdrug response
rs15848232547:87,133,165C/Tdrug response
rs8873088197:87,133,180C/Tdrug response
rs15848232907:87,133,196T/Gdrug response
rs14141731647:87,133,261G/Adrug response
rs15848233687:87,133,287A/Gdrug response
rs15848233777:87,133,292A/Gdrug response
rs5497532907:87,133,336G/Adrug response
rs38427:87,133,366T/C3 prime UTR variantdrug response
rs15848234707:87,133,370T/Gdrug response
rs15848234737:87,133,373T/Adrug response
rs15848234807:87,133,376C/Adrug response
rs12013552387:87,133,380T/Gdrug response
rs15848234997:87,133,385G/Adrug response
rs15848235197:87,133,398C/Gdrug response
rs15848235317:87,133,404C/Tdrug response
rs15848235417:87,133,405T/Cdrug response
rs15848235947:87,133,468C/Gdrug response
rs170647:87,133,470T/Adrug response
rs15848236427:87,133,490T/Gdrug response
rs15848236517:87,133,495C/Gdrug response
rs15848236557:87,133,496T/Gdrug response
rs7499040977:87,133,531A/Cdrug response
rs15848237177:87,133,539A/Gdrug response
rs2020266007:87,133,546A/Gdrug response
rs15848237457:87,133,565G/Adrug response
rs1379969147:87,133,567G/Tuncertain significance
rs21170531607:87,133,576C/Tuncertain significance
rs14571915187:87,133,601A/Tdrug response
rs14154475537:87,133,602T/Gdrug response
rs15848238117:87,133,603A/Cdrug response
rs7711007077:87,133,633G/Auncertain significance
rs1494825367:87,133,634C/Tlikely benign
rs15848238667:87,133,644T/Cdrug response
rs283642747:87,133,651C/Tmissense variantbenign
rs13734557867:87,133,653C/Tdrug response
rs22350517:87,133,655G/Clikely benign
rs2016099307:87,133,656C/Tdrug response
rs2006371947:87,133,695G/Amissense variant
rs5633753877:87,133,705G/Auncertain significance
rs15848240097:87,133,711C/Tdrug response
rs7573944987:87,133,714T/Cdrug response
rs15848240607:87,133,723A/Tdrug response
rs12817462647:87,133,729G/Auncertain significance
rs13449720137:87,133,737C/Guncertain significance
rs15848241317:87,133,753C/Tdrug response
rs15848241537:87,133,759G/Tdrug response
rs15848241597:87,133,761A/Cdrug response
rs15848241827:87,133,776A/Cdrug response
rs15848261857:87,135,183A/Gdrug response
rs15848263107:87,135,248C/Tdrug response
rs15848263497:87,135,278C/Tdrug response
rs7644635837:87,135,295G/Tdrug response
rs1996760987:87,135,302G/Auncertain significance
rs14213519177:87,135,305G/Adrug response
rs15848264227:87,135,306T/Gdrug response
rs15848264337:87,135,308T/Adrug response
rs15848264857:87,135,326G/Adrug response
rs15848265217:87,135,348A/Tdrug response
rs15848265247:87,135,370G/Adrug response
rs15848266077:87,135,425G/Adrug response
rs15848266517:87,135,443T/Gdrug response
rs7623746137:87,138,573A/Gdrug response
rs12552168137:87,138,586C/Tdrug response
rs10456427:87,138,645A/Gsynonymous variantdrug response
rs20325837:87,138,645G/Aintronic
rs22291077:87,138,659A/Tmissense variantlikely benign
rs7735977577:87,138,668G/Auncertain significance
rs347486557:87,138,684G/Abenign
rs7630917877:87,138,695C/Tuncertain significance
rs15848295687:87,138,703C/Adrug response
rs7582121807:87,138,707A/Tdrug response
rs12534620047:87,138,710C/Tdrug response
rs15848296027:87,138,725C/Tdrug response
rs15848296087:87,138,728G/Cuncertain significance
rs14559496027:87,138,729G/Cdrug response
rs357303087:87,138,758A/Gmissense variant
rs558526207:87,138,760T/Gconflicting classifications of pathogenicity
rs12906871327:87,138,834G/Adrug response
rs610401227:87,138,847G/Adrug response
rs15848298517:87,138,851C/Tdrug response
rs9493430487:87,138,858A/Gdrug response
rs15848298727:87,138,863C/Tdrug response
rs10022057:87,141,174G/T
rs1914795697:87,141,310C/Tintron variant
rs1417557207:87,144,515C/Adrug response
rs7462054987:87,144,520C/Adrug response
rs15848346177:87,144,545A/Cdrug response
rs15848346237:87,144,548A/Cdrug response
rs7768273287:87,144,552T/Cdrug response
rs2005140287:87,144,582G/Cuncertain significance
rs13777954237:87,144,594C/Tdrug response
rs15848347967:87,144,605C/Tdrug response
rs3737898687:87,144,622C/Gdrug response
rs15848348487:87,144,628A/Cdrug response
rs3680962417:87,144,634C/Tdrug response
rs7619142667:87,144,642C/Adrug response
rs15848348997:87,144,644T/Cdrug response

Showing 100 of 677 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.