ADAMTS6

ADAM metallopeptidase with thrombospondin type 1 motif 6

Summary

This gene encodes a member of the ADAMTS (a disintegrin and metalloproteinase with thrombospondin motifs) protein family. Members of the family share several distinct protein modules, including a propeptide region, a metalloproteinase domain, a disintegrin-like domain, and a thrombospondin type 1 (TS) motif. Individual members of this family differ in the number of C-terminal TS motifs, and some have unique C-terminal domains. The encoded preproprotein is proteolytically processed to generate the mature enzyme. Expression of this gene may be regulated by the cytokine TNF-alpha. [provided by RefSeq, Mar 2016]

Known Variants70 total

rsidPosition (GRCh37)AllelesClassClinVar
rs47000765:64,444,070T/Cdownstream gene variant
rs172067795:64,447,777C/A
rs7156765:64,450,473A/Tintron variant
rs64497745:64,451,301G/T
rs77028875:64,451,583C/Tintron variant
rs15592565:64,452,205A/Cintron variant
rs131530055:64,460,096T/G
rs7463861445:64,466,459T/Cuncertain significance
rs1475302675:64,466,506C/Tuncertain significance
rs5373439645:64,466,540C/Guncertain significance
rs5538019755:64,468,675G/Alikely benign
rs2009638305:64,468,714C/Tuncertain significance
rs7691907435:64,468,715G/Auncertain significance
rs5557378205:64,468,721G/Cuncertain significance
rs24787708945:64,468,769T/Cuncertain significance
rs7683474615:64,468,785C/Guncertain significance
rs12726123015:64,483,913C/Tlikely pathogenic
rs5625136145:64,483,962C/Tuncertain significance
rs1434108315:64,484,026C/Guncertain significance
rs3710441515:64,511,285T/Cuncertain significance
rs777120435:64,520,165T/Cbenign
rs7800095715:64,520,837C/Tuncertain significance
rs799633795:64,520,851C/Auncertain significance
rs24791797595:64,521,965C/Guncertain significance
rs14600203615:64,522,040A/Cuncertain significance
rs131837915:64,534,641C/Aintron variant
rs24792955265:64,538,003C/Guncertain significance
rs5422933435:64,538,014C/Tuncertain significance
rs24792958305:64,538,017G/Auncertain significance
rs783067135:64,542,378T/Cdownstream gene variant
rs125178765:64,550,321A/Gupstream gene variant
rs1467404545:64,556,482C/Guncertain significance
rs24795089205:64,558,665A/Cuncertain significance
rs7705016915:64,558,687C/Guncertain significance
rs64497785:64,563,813G/Aintron variant
rs117439605:64,568,555C/Tintron variant
rs7632651965:64,569,168C/Tuncertain significance
rs24797973565:64,587,236C/Tuncertain significance
rs3690127605:64,587,272T/Cuncertain significance
rs3729733725:64,595,833T/Cuncertain significance
rs14055486295:64,595,834C/Auncertain significance
rs10484798895:64,595,863T/Cuncertain significance
rs12862581445:64,595,908T/Cuncertain significance
rs43231875:64,604,013T/Cintron variant
rs667244255:64,605,753T/Cintron variant
rs105149795:64,607,614G/A
rs17464932195:64,625,265C/Tuncertain significance
rs17464955905:64,625,281G/Auncertain significance
rs23071215:64,625,512C/Tintron variant
rs100715075:64,638,339T/Cintron variant
rs168937175:64,644,871C/Tintron variant
rs134362435:64,652,495T/Cintron variant
rs1852066925:64,671,126A/T
rs1133919215:64,671,570C/Tintron variant
rs77160465:64,684,894G/Tintron variant
rs623707025:64,693,485C/Tintron variant
rs119602935:64,699,190A/Tintron variant
rs24809983025:64,748,047A/Cuncertain significance
rs10291238625:64,748,646C/Tuncertain significance
rs7470434265:64,748,677T/Cuncertain significance
rs3681912655:64,748,724G/Alikely benign
rs15615628335:64,756,020T/Auncertain significance
rs1415873205:64,756,164T/Clikely benign
rs7508222695:64,766,630A/Guncertain significance
rs24810965645:64,766,696T/Guncertain significance
rs617364545:64,766,798G/Alikely benign
rs17603922405:64,766,823C/Tuncertain significance
rs13114651255:64,766,840A/Cuncertain significance
rs7790661935:64,769,423C/Auncertain significance
rs14330911365:64,769,465C/Guncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.