AFF1

ALF transcription elongation factor 1

Summary

This gene encodes a member of the AF4/ lymphoid nuclear protein related to the Fragile X E syndrome (FRAXE) family of proteins, which have been implicated in human childhood lymphoblastic leukemia, fragile chromosome X intellectual disability, and ataxia. It is the prevalent mixed-lineage leukemia fusion gene associated with spontaneous acute lymphoblastic leukemia. Members of this family have three conserved domains: an N-terminal homology domain, an AF4/ lymphoid nuclear protein domain, and a C-terminal homology domain. The protein functions as a regulator of RNA polymerase II-mediated transcription through elongation and chromatin remodeling functions. Through RNA interference screens, this gene has been shown to promote the expression of CD133, a plasma membrane glycoprotein required for leukemia cell survival. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jul 2017]

Known Variants145 total

rsidPosition (GRCh37)AllelesClassClinVar
rs792430124:87,860,512T/Cregulatory region variant
rs801993414:87,860,514T/Gregulatory region variant
rs726677374:87,876,416C/Tintron variant
rs9031170114:87,879,485T/G
rs9658244:87,880,096G/C
rs347458734:87,882,815A/Cregulatory region variant
rs76938894:87,885,401G/C
rs1810032764:87,890,628C/Tintron variant
rs559131644:87,898,930T/A
rs177523074:87,899,285T/Gregulatory region variant
rs340777454:87,905,696G/Tintron variant
rs131263344:87,909,890A/Gintron variant
rs1431522284:87,913,610C/Tregulatory region variant
rs5297111504:87,915,951T/C
rs1495806784:87,919,711T/Cintron variant
rs131236214:87,921,757C/G
rs3406354:87,931,404A/Gregulatory region variant
rs46938014:87,932,099C/Tregulatory region variant
rs564061254:87,940,205G/Tintron variant
rs563903634:87,943,087G/Aintron variant
rs726677574:87,946,994C/Aregulatory region variant
rs726677594:87,952,199C/A
rs623065084:87,956,674C/Tintron variant
rs3406304:87,958,395G/Aregulatory region variant
rs726677654:87,965,942G/Aregulatory region variant
rs2012129464:87,967,323A/Guncertain significance
rs3729830274:87,967,326A/Guncertain significance
rs7459200654:87,967,359A/Guncertain significance
rs76891674:87,967,399A/Gbenign
rs7774760844:87,967,848C/Tuncertain significance
rs7708380394:87,967,872G/Auncertain significance
rs13569236184:87,967,902A/Guncertain significance
rs5605352904:87,967,926C/Tuncertain significance
rs3739487944:87,967,943C/Tuncertain significance
rs3681340004:87,967,944G/Auncertain significance
rs1505086964:87,967,977C/Tuncertain significance
rs1500659854:87,968,067C/Tuncertain significance
rs14316829814:87,968,220C/Guncertain significance
rs1436733124:87,968,254C/Tlikely benign
rs25478609164:87,968,304C/Tuncertain significance
rs11569730814:87,968,402G/Alikely benign
rs7510200974:87,968,409G/Alikely benign
rs7538690934:87,968,427A/Glikely benign
rs13318574764:87,968,492A/Guncertain significance
rs1486175914:87,968,562C/Tuncertain significance
rs2009465634:87,968,568A/Tuncertain significance
rs7540353044:87,968,670C/Tuncertain significance
rs7481441544:87,968,680A/Cuncertain significance
rs8676657724:87,968,696C/Tuncertain significance
rs1411268124:87,968,728G/Tuncertain significance
rs3749485234:87,968,729C/Tuncertain significance
rs1401774064:87,968,738T/Auncertain significance
rs8671964:87,971,600G/Cintron variant
rs20071324:87,972,585G/C
rs76608834:87,982,876C/A
rs119464814:87,984,610C/Tintron variant
rs100189044:87,986,206G/T
rs131203014:87,986,395C/Tintron variant
rs2366794:87,986,601A/T
rs22809534:87,988,590C/Tintron variant
rs176056154:87,996,745G/Aintron variant
rs2369844:88,008,614G/Aintron variant
rs3751679904:88,008,832C/T
rs12182609824:88,011,140T/Cuncertain significance
rs3702988684:88,011,172A/Guncertain significance
rs7591264804:88,011,176A/Guncertain significance
rs1135020774:88,011,210T/Cbenign
rs1873825754:88,011,230C/Tlikely benign
rs17243440094:88,012,961G/Auncertain significance
rs1458772834:88,016,116G/Alikely benign
rs1514504:88,016,514G/T
rs3424544:88,021,500T/G
rs606952584:88,022,709C/Tintron variant
rs716074044:88,024,333T/Aintron variant
rs24761186844:88,026,975C/Guncertain significance
rs16749994:88,027,650G/Aintron variant
rs7783470054:88,029,313C/Auncertain significance
rs17261156354:88,029,349A/Tuncertain significance
rs1417209054:88,029,376C/Guncertain significance
rs7685546194:88,029,453A/Tuncertain significance
rs4421774:88,030,261G/C
rs759218544:88,032,096T/Aintron variant
rs21497666304:88,035,579C/Tuncertain significance
rs2019932294:88,035,586C/Tlikely benign
rs17268643974:88,035,601C/Guncertain significance
rs1492559144:88,035,624C/Tuncertain significance
rs7668193774:88,035,625G/Auncertain significance
rs7707041844:88,035,664G/Auncertain significance
rs7636141534:88,035,706C/Guncertain significance
rs7543606704:88,035,720C/Tuncertain significance
rs3722995294:88,035,732G/Auncertain significance
rs1165370984:88,035,755G/Alikely benign
rs24762096784:88,035,766A/Guncertain significance
rs1401967704:88,035,804G/Cuncertain significance
rs7545399314:88,035,840T/Cuncertain significance
rs14347966164:88,035,850C/Tuncertain significance
rs1130260654:88,035,864A/Tlikely benign
rs7505550964:88,035,888G/Cuncertain significance
rs7559103684:88,035,901A/Guncertain significance
rs14495327244:88,035,934C/Tuncertain significance

Showing 100 of 145 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.