ARSB

arylsulfatase B

Summary

Arylsulfatase B encoded by this gene belongs to the sulfatase family. The arylsulfatase B homodimer hydrolyzes sulfate groups of N-Acetyl-D-galactosamine, chondriotin sulfate, and dermatan sulfate. The protein is targeted to the lysozyme. Mucopolysaccharidosis type VI is an autosomal recessive lysosomal storage disorder resulting from a deficiency of arylsulfatase B. Two alternatively spliced transcript variants encoding distinct isoforms have been found for this gene. [provided by RefSeq, Dec 2016]

Known Variants725 total

rsidPosition (GRCh37)AllelesClassClinVar
rs168758875:78,073,025T/Clikely benign
rs117507745:78,073,039A/Cuncertain significance
rs8860607775:78,073,046A/Cuncertain significance
rs8860607785:78,073,057A/Guncertain significance
rs8860607795:78,073,068T/Cuncertain significance
rs14256060695:78,073,073C/Tuncertain significance
rs5602538235:78,073,173A/Guncertain significance
rs30882475:78,073,245A/Cbenign
rs1168260655:78,073,361A/Gbenign
rs12259064885:78,073,389A/Tuncertain significance
rs13900089385:78,073,436G/Tuncertain significance
rs1416672085:78,073,512C/Tuncertain significance
rs1839182065:78,073,513G/Auncertain significance
rs1888598455:78,073,536C/Tuncertain significance
rs10439010415:78,073,540G/Auncertain significance
rs8860607805:78,073,548T/Cuncertain significance
rs1471705055:78,073,566T/Cbenign
rs5692545285:78,073,612C/Tuncertain significance
rs17488112145:78,073,627A/Cuncertain significance
rs5480936055:78,073,642T/Auncertain significance
rs9639441565:78,073,649T/Cuncertain significance
rs9756587245:78,073,661C/Tuncertain significance
rs11743873115:78,073,694A/Tuncertain significance
rs8679237835:78,073,695T/Auncertain significance
rs8680666755:78,073,696T/Auncertain significance
rs133543245:78,073,812T/Cconflicting classifications of pathogenicity
rs8860607825:78,073,933G/Auncertain significance
rs5325139605:78,073,969C/Tuncertain significance
rs1455859435:78,073,977T/Clikely benign
rs9506477005:78,074,056A/Tuncertain significance
rs14636426315:78,074,062G/Auncertain significance
rs17488258885:78,074,065G/Auncertain significance
rs17488275725:78,074,128T/Auncertain significance
rs8860607835:78,074,140C/Tuncertain significance
rs77049395:78,074,198C/Abenign
rs1130599355:78,074,207C/Tuncertain significance
rs8789265075:78,074,231G/Auncertain significance
rs1498546785:78,074,269T/Cuncertain significance
rs355977825:78,074,585C/Tconflicting classifications of pathogenicity
rs8671001565:78,074,610C/Tuncertain significance
rs1889988315:78,074,626G/Tuncertain significance
rs8860607865:78,074,707G/Auncertain significance
rs8860607875:78,074,721G/Cuncertain significance
rs557104525:78,074,751A/Gbenign
rs791661905:78,074,800C/Tuncertain significance
rs5555810695:78,074,833G/Auncertain significance
rs1465847845:78,074,847T/Cuncertain significance
rs8860607885:78,074,860A/Tuncertain significance
rs9749429255:78,074,894C/Auncertain significance
rs7545665:78,074,918C/Abenign
rs8860607895:78,074,934G/Auncertain significance
rs8860607905:78,074,944G/Cuncertain significance
rs7545675:78,074,963G/Tbenign
rs8860607915:78,075,051A/Guncertain significance
rs1167537855:78,075,067G/Tuncertain significance
rs8860607925:78,075,073C/Tuncertain significance
rs1410019945:78,075,074C/Tuncertain significance
rs1906327565:78,075,226G/Tuncertain significance
rs8860607935:78,075,230G/Auncertain significance
rs1448187355:78,075,255T/Cuncertain significance
rs9249981635:78,075,287G/Auncertain significance
rs2012847665:78,075,298G/Auncertain significance
rs7771607805:78,075,410G/Auncertain significance
rs8860607945:78,075,427A/Tuncertain significance
rs5344805715:78,075,585G/Cuncertain significance
rs8860607955:78,075,601C/Auncertain significance
rs7578575435:78,075,602G/Auncertain significance
rs8860607965:78,075,612C/Tuncertain significance
rs17488767445:78,075,800T/Cuncertain significance
rs9704653235:78,075,836A/Tuncertain significance
rs12346194235:78,075,880T/Guncertain significance
rs5617187205:78,076,008T/Cuncertain significance
rs737700195:78,076,018T/Cbenign
rs1813213495:78,076,054C/Tuncertain significance
rs21730125:78,076,160T/Clikely benign
rs15540696555:78,076,221T/Cpathogenic
rs15540696575:78,076,222A/Guncertain significance
rs24788180605:78,076,227C/Tuncertain significance
rs15540696595:78,076,230G/Cuncertain significance
rs15809609415:78,076,232G/Tlikely benign
rs10283373115:78,076,238C/Tlikely benign
rs24788181175:78,076,241C/Glikely benign
rs21126170065:78,076,244A/Glikely benign
rs21126170155:78,076,247G/Tlikely benign
rs15540696615:78,076,260C/Tconflicting classifications of pathogenicity
rs7500931685:78,076,262G/Alikely benign
rs8893447085:78,076,263C/Tuncertain significance
rs7555769845:78,076,264G/Auncertain significance
rs17488906745:78,076,265G/Alikely benign
rs12331080735:78,076,268G/Tuncertain significance
rs11584010035:78,076,274T/Glikely benign
rs2012341535:78,076,276C/Tuncertain significance
rs7555503455:78,076,277A/Clikely benign
rs12514380625:78,076,283G/Tpathogenic
rs2019287775:78,076,288C/Tuncertain significance
rs5281578335:78,076,289G/Aconflicting classifications of pathogenicity
rs21126171075:78,076,292G/Alikely benign
rs15540696635:78,076,307G/Auncertain significance
rs7711134725:78,076,315G/Apathogenic
rs24788184365:78,076,316T/Clikely benign

Showing 100 of 725 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.