ATP6V0D2

ATPase H+ transporting V0 subunit d2

Summary

Predicted to enable proton-transporting ATPase activity, rotational mechanism. Predicted to be involved in vacuolar acidification and vacuolar transport. Located in apical plasma membrane. Part of vacuolar proton-transporting V-type ATPase complex. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants53 total

rsidPosition (GRCh37)AllelesClassClinVar
rs746676358:87,111,154C/Tlikely benign
rs7572147408:87,111,236A/Guncertain significance
rs25367915788:87,111,308T/Cuncertain significance
rs7807540578:87,111,332T/Guncertain significance
rs2017712918:87,111,368G/Abenign
rs78360038:87,111,515A/Cbenign
rs732573358:87,125,628G/Abenign
rs9388995358:87,126,007T/Cuncertain significance
rs7752477518:87,126,016T/Cuncertain significance
rs1494851968:87,126,063C/Tuncertain significance
rs176027808:87,126,151G/Abenign
rs176606828:87,126,178G/Cbenign
rs117758658:87,147,765A/Gintron variant
rs24663268:87,151,606G/Cbenign
rs1918441458:87,151,712T/Cuncertain significance
rs7789924708:87,151,823C/Tuncertain significance
rs7586259388:87,151,837A/Guncertain significance
rs2020913838:87,153,696T/Guncertain significance
rs1398320368:87,153,697G/Auncertain significance
rs25368230108:87,153,726A/Cuncertain significance
rs558387458:87,153,904T/Cbenign
rs176038978:87,155,037G/Abenign
rs14837798:87,155,094T/Cbenign
rs755948988:87,155,225C/Tbenign
rs102830728:87,160,417T/Cregulatory region variant
rs670385518:87,162,098T/Abenign
rs7541673668:87,162,398A/Cuncertain significance
rs7589800138:87,162,423A/Guncertain significance
rs9325952998:87,162,426C/Tuncertain significance
rs3731222368:87,162,434G/Tuncertain significance
rs1998961828:87,162,444A/Guncertain significance
rs1873387958:87,162,446C/Tuncertain significance
rs5496119578:87,162,459G/Auncertain significance
rs1435878138:87,162,510A/Guncertain significance
rs100947448:87,162,515G/Abenign
rs70117248:87,162,790G/Abenign
rs70117258:87,162,794G/Tbenign
rs49904038:87,163,455T/Cbenign
rs677050498:87,163,496C/Abenign
rs1408242428:87,163,701A/Guncertain significance
rs5659424948:87,163,729G/Auncertain significance
rs7457143258:87,163,742A/Clikely benign
rs1385735208:87,163,752G/Auncertain significance
rs1506985198:87,163,770G/Tbenign
rs775952588:87,163,984C/Tlikely benign
rs593697948:87,164,053C/Tbenign
rs117806338:87,164,511C/Tdownstream gene variant
rs100951078:87,164,886T/Cbenign
rs105048208:87,165,011T/Cbenign
rs1423553028:87,165,071C/Aconflicting classifications of pathogenicity
rs7757199018:87,165,087G/Auncertain significance
rs18191769628:87,165,115A/Guncertain significance
rs7522468248:87,165,175C/Tuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.