BACE1

beta-secretase 1

Summary

This gene encodes a member of the peptidase A1 family of aspartic proteases. Alternative splicing results in multiple transcript variants, at least one of which encodes a preproprotein that is proteolytically processed to generate the mature protease. This transmembrane protease catalyzes the first step in the formation of amyloid beta peptide from amyloid precursor protein. Amyloid beta peptides are the main constituent of amyloid beta plaques, which accumulate in the brains of human Alzheimer's disease patients. [provided by RefSeq, Nov 2015]

Known Variants37 total

rsidPosition (GRCh37)AllelesClassClinVar
rs104796411:117,156,893G/T
rs53586011:117,159,878A/Tdownstream gene variant
rs20221981711:117,160,321C/Tsynonymous variant
rs13864409311:117,160,329G/Auncertain significance
rs253986915711:117,160,412G/Tuncertain significance
rs36901439711:117,160,415A/Guncertain significance
rs76331790511:117,160,422T/Cuncertain significance
rs253986926011:117,160,427G/Tuncertain significance
rs146972636711:117,160,428T/Cuncertain significance
rs14258194911:117,160,435A/Tuncertain significance
rs253986956411:117,160,478G/Auncertain significance
rs36825874911:117,161,242G/Auncertain significance
rs76831507411:117,161,654C/Tuncertain significance
rs75195566511:117,161,746C/Tuncertain significance
rs75660088511:117,161,764G/Auncertain significance
rs203444548811:117,162,484G/Auncertain significance
rs75177366011:117,163,782C/Auncertain significance
rs63840511:117,163,824C/Gsynonymous variant
rs134276962411:117,163,840T/Guncertain significance
rs77588026411:117,163,846C/Tuncertain significance
rs57150869211:117,163,847G/Auncertain significance
rs77375297911:117,163,874T/Cuncertain significance
rs253988832611:117,164,615T/Guncertain significance
rs253988842711:117,164,642C/Tuncertain significance
rs96923031811:117,166,007T/Cuncertain significance
rs253989388911:117,166,016G/Tuncertain significance
rs75281500811:117,167,628G/Tuncertain significance
rs54843267611:117,171,454T/G
rs68021011:117,172,820T/A
rs14209333711:117,177,383C/Tregulatory region variant
rs52549311:117,182,708T/Gupstream gene variant
rs75992460211:117,186,258G/Auncertain significance
rs76464228311:117,186,321A/Guncertain significance
rs91948498211:117,186,394C/Guncertain significance
rs100106779611:117,186,415C/Auncertain significance
rs120196791511:117,186,478T/Clikely benign
rs493836911:117,188,120C/Tupstream gene variant

Gene information from NCBI Gene. Variant classifications from ClinVar.