BLMH

bleomycin hydrolase

Summary

Bleomycin hydrolase (BMH) is a cytoplasmic cysteine peptidase that is highly conserved through evolution; however, the only known activity of the enzyme is metabolic inactivation of the glycopeptide bleomycin (BLM), an essential component of combination chemotherapy regimens for cancer. The protein contains the signature active site residues of the cysteine protease papain superfamily. [provided by RefSeq, Jul 2008]

Known Variants29 total

rsidPosition (GRCh37)AllelesClassClinVar
rs105056517:28,576,076T/Cmissense variantbenign
rs14822597117:28,576,085C/Tuncertain significance
rs11619428917:28,576,106C/Tuncertain significance
rs18959889017:28,578,014A/Gupstream gene variant
rs14889419817:28,579,420A/Gdownstream gene variant
rs7507661517:28,580,395C/Tdownstream gene variant
rs18112694417:28,584,612C/Tintron variant
rs379480617:28,586,903T/Gintron variant
rs14653450017:28,587,761C/Tintron variant
rs212978517:28,590,530T/Cintron variant
rs13788171917:28,598,294C/Astop gained
rs250963764617:28,598,348G/Cuncertain significance
rs36808846917:28,599,609T/Cuncertain significance
rs75451331917:28,599,613A/Cuncertain significance
rs37231078517:28,599,778G/Auncertain significance
rs75842840317:28,599,805A/Guncertain significance
rs250963882617:28,599,875T/Cuncertain significance
rs54299669917:28,599,877T/Cuncertain significance
rs86835218917:28,601,172G/Auncertain significance
rs18553358017:28,606,498G/Aintron variant
rs14023342917:28,608,636A/Gintron variant
rs250964551117:28,612,456C/Tuncertain significance
rs135657567417:28,614,937G/Cuncertain significance
rs76072124517:28,614,940C/Tlikely benign
rs75577663917:28,616,497C/Tuncertain significance
rs14354476417:28,618,350T/Clikely benign
rs159767012717:28,618,413G/Auncertain significance
rs75507778417:28,618,497T/Auncertain significance
rs15014429017:28,618,517G/Auncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.