CEP170

centrosomal protein 170

Summary

The product of this gene is a component of the centrosome, a non-membraneous organelle that functions as the major microtubule-organizing center in animal cells. During interphase, the encoded protein localizes to the sub-distal appendages of mature centrioles, which are microtubule-based structures thought to help organize centrosomes. During mitosis, the protein associates with spindle microtubules near the centrosomes. The protein interacts with and is phosphorylated by polo-like kinase 1, and functions in maintaining microtubule organization and cell morphology. The human genome contains a putative transcribed pseudogene. Several alternatively spliced transcript variants of this gene have been found, but the full-length nature of some of these variants has not been determined. [provided by RefSeq, Jul 2008]

Known Variants89 total

rsidPosition (GRCh37)AllelesClassClinVar
rs13772655071:243,289,903T/Cuncertain significance
rs20537258461:243,289,919G/Cuncertain significance
rs7795065341:243,289,924G/Auncertain significance
rs7684889311:243,289,936C/Tuncertain significance
rs5610985241:243,289,956G/Auncertain significance
rs120477741:243,299,436T/Abenign
rs12383967431:243,299,469A/Guncertain significance
rs12859749241:243,299,470T/Cuncertain significance
rs7688005871:243,299,488T/Cuncertain significance
rs7744323661:243,299,503C/Tuncertain significance
rs11777376551:243,299,519A/Tuncertain significance
rs20556388841:243,303,319A/Guncertain significance
rs7742606501:243,303,351T/Cuncertain significance
rs20556458481:243,303,367T/Auncertain significance
rs25464108971:243,305,749C/Tuncertain significance
rs1839361011:243,319,561G/Alikely benign
rs21484637261:243,319,585G/Cuncertain significance
rs1481254171:243,319,611T/Cbenign
rs5635151851:243,319,625C/Auncertain significance
rs7642581551:243,319,635G/Auncertain significance
rs20583044011:243,327,687A/Guncertain significance
rs13372535911:243,327,691G/Cuncertain significance
rs12568104921:243,327,712T/Cuncertain significance
rs8922785801:243,327,754T/Cuncertain significance
rs7538318591:243,327,774G/Auncertain significance
rs2011675611:243,327,785G/Alikely benign
rs11786040411:243,327,802G/Auncertain significance
rs1834450021:243,327,936C/Guncertain significance
rs7670935251:243,328,023G/Auncertain significance
rs3716325641:243,328,041G/Auncertain significance
rs25467309391:243,328,116C/Auncertain significance
rs7604374231:243,328,144T/Guncertain significance
rs25467322931:243,328,147T/Cuncertain significance
rs14661897311:243,328,227C/Auncertain significance
rs5338264071:243,328,368T/Cuncertain significance
rs7477653781:243,328,537G/Auncertain significance
rs7667245301:243,328,588G/Auncertain significance
rs2010827521:243,328,635C/Tlikely benign
rs7501491311:243,328,726G/Auncertain significance
rs7469379221:243,328,740A/Guncertain significance
rs9432069801:243,328,779T/Guncertain significance
rs7495538191:243,328,788T/Auncertain significance
rs7713108691:243,328,794C/Auncertain significance
rs12963591131:243,328,869T/Guncertain significance
rs25467556401:243,328,902G/Cuncertain significance
rs7568877831:243,328,993C/Tuncertain significance
rs13337986291:243,329,008C/Guncertain significance
rs7533503711:243,329,068T/Guncertain significance
rs13238459001:243,329,072C/Guncertain significance
rs3731356781:243,329,085G/Auncertain significance
rs7711895951:243,329,109G/Cuncertain significance
rs7659754391:243,329,159C/Tuncertain significance
rs5681500191:243,329,160A/Guncertain significance
rs3715325451:243,329,200G/Cuncertain significance
rs7493910591:243,329,206C/Guncertain significance
rs2001283781:243,329,349C/Tuncertain significance
rs2010856751:243,329,376C/Tuncertain significance
rs25468211121:243,332,931A/Cuncertain significance
rs9125165361:243,332,934C/Guncertain significance
rs7644377751:243,332,942G/Auncertain significance
rs3743842951:243,332,977T/Cuncertain significance
rs3729332331:243,333,012C/Guncertain significance
rs7453121581:243,333,029G/Auncertain significance
rs7650507861:243,336,070C/Auncertain significance
rs27891111:243,346,404T/G
rs7755925651:243,349,132C/Guncertain significance
rs1904697771:243,349,352C/Tuncertain significance
rs3707693041:243,349,374T/Auncertain significance
rs7660826321:243,349,604A/Guncertain significance
rs7566527021:243,349,629G/Auncertain significance
rs2009466561:243,349,655C/Tuncertain significance
rs25470191341:243,349,706C/Tuncertain significance
rs9573694211:243,354,440C/Tuncertain significance
rs3726230141:243,354,503A/Guncertain significance
rs7716471731:243,354,508T/Cuncertain significance
rs13552005761:243,354,554C/Tuncertain significance
rs25470899241:243,354,563G/Tuncertain significance
rs9727470111:243,354,615A/Tuncertain significance
rs14832687611:243,354,637G/Auncertain significance
rs25470939151:243,354,694G/Auncertain significance
rs3746801511:243,362,485T/Cuncertain significance
rs9843620371:243,363,896A/Tuncertain significance
rs21719731:243,383,636A/Tupstream gene variant
rs1851889391:243,385,102T/Cuncertain significance
rs25474412021:243,385,112G/Cuncertain significance
rs15654401:243,387,788G/Aupstream gene variant
rs109269731:243,388,370A/Tintron variant
rs7760343671:243,388,539C/Tuncertain significance
rs715373311:243,418,182C/G

Gene information from NCBI Gene. Variant classifications from ClinVar.