COP1

COP1 E3 ubiquitin ligase

Summary

Enables ubiquitin protein ligase activity. Involved in positive regulation of proteasomal ubiquitin-dependent protein catabolic process; proteasome-mediated ubiquitin-dependent protein catabolic process; and response to ionizing radiation. Part of Cul4A-RING E3 ubiquitin ligase complex. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants44 total

rsidPosition (GRCh37)AllelesClassClinVar
rs9761029571:175,916,369T/Guncertain significance
rs15714143511:175,956,103C/Tlikely benign
rs14645692671:175,956,169A/Tuncertain significance
rs5577830321:175,957,433T/Cuncertain significance
rs2019051411:175,957,444T/Cuncertain significance
rs7498209461:175,958,570A/Cuncertain significance
rs1115313721:175,958,578T/Cbenign
rs358463791:175,968,013G/C
rs1841470741:175,974,794G/Aintron variant
rs10414152661:176,012,392C/Tlikely benign
rs14526114611:176,012,893C/Tuncertain significance
rs12988876871:176,015,440C/Tuncertain significance
rs782757271:176,027,200G/Aintron variant
rs11809425481:176,050,309T/Cuncertain significance
rs1489501581:176,050,414C/Tuncertain significance
rs8790199981:176,050,430G/Alikely benign
rs5571680881:176,050,431A/Glikely benign
rs25467432441:176,054,914G/Auncertain significance
rs25467452621:176,055,023T/Cuncertain significance
rs11628206251:176,085,790G/Tuncertain significance
rs7454816391:176,085,803G/Tuncertain significance
rs25471775601:176,104,203G/Cuncertain significance
rs412661101:176,104,219T/Cbenign
rs751244171:176,105,631C/Gbenign
rs25471902081:176,105,652A/Tuncertain significance
rs1464477271:176,110,620G/Cregulatory region variant
rs16920112371:176,118,186T/Cuncertain significance
rs1393731711:176,118,187C/Glikely benign
rs13852408281:176,132,021T/Cuncertain significance
rs13308618741:176,132,106T/Cuncertain significance
rs3700917591:176,132,994A/Guncertain significance
rs1386682281:176,145,082C/Tuncertain significance
rs127555071:176,164,865T/Cintron variant
rs7722312731:176,175,723C/Tuncertain significance
rs7799645401:176,175,765G/Auncertain significance
rs13444826341:176,175,828C/Guncertain significance
rs7787067411:176,175,864G/Auncertain significance
rs7691185921:176,175,913C/Tuncertain significance
rs17009102851:176,175,927C/Tuncertain significance
rs25476955551:176,175,933A/Cuncertain significance
rs7651862571:176,176,014G/Auncertain significance
rs5288472901:176,176,071C/Tuncertain significance
rs7514997961:176,176,084A/Tuncertain significance
rs8931916281:176,176,095G/Auncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.