FMO1

flavin containing dimethylaniline monoxygenase 1

Summary

Metabolic N-oxidation of the diet-derived amino-trimethylamine (TMA) is mediated by flavin-containing monooxygenase and is subject to an inherited FMO3 polymorphism in man resulting in a small subpopulation with reduced TMA N-oxidation capacity resulting in fish odor syndrome Trimethylaminuria. Three forms of the enzyme, FMO1 found in fetal liver, FMO2 found in adult liver, and FMO3 are encoded by genes clustered in the 1q23-q25 region. Flavin-containing monooxygenases are NADPH-dependent flavoenzymes that catalyzes the oxidation of soft nucleophilic heteroatom centers in drugs, pesticides, and xenobiotics. Several transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Sep 2013]

Known Variants36 total

rsidPosition (GRCh37)AllelesClassClinVar
rs25253194361:171,227,231C/Tuncertain significance
rs1825254821:171,227,237G/Auncertain significance
rs25253196111:171,227,245A/Guncertain significance
rs12153518191:171,227,293G/Auncertain significance
rs3767425121:171,227,348G/Cuncertain significance
rs66745961:171,235,088A/Tintron variant
rs2002102091:171,236,689T/Cuncertain significance
rs7691410011:171,236,694G/Auncertain significance
rs2021094031:171,236,709C/Auncertain significance
rs7640990491:171,236,757T/Cuncertain significance
rs283603971:171,244,541G/Tuncertain significance
rs7654216971:171,244,618A/Guncertain significance
rs283604071:171,247,858T/Cbenign
rs2017849821:171,247,877C/Tuncertain significance
rs1458495411:171,247,899T/Auncertain significance
rs3727854571:171,247,903C/Tuncertain significance
rs3771690791:171,247,904G/Auncertain significance
rs1463296121:171,249,957G/Alikely benign
rs7799336821:171,249,971T/Cuncertain significance
rs3770449001:171,249,985C/Auncertain significance
rs1502689681:171,250,049T/Clikely benign
rs7711967771:171,250,076T/Cuncertain significance
rs283604201:171,251,268T/Cbenign
rs1454153381:171,251,347A/Guncertain significance
rs1161909641:171,251,367C/Tlikely benign
rs283604211:171,251,407A/Gbenign
rs8659523031:171,251,449G/Cuncertain significance
rs7520720221:171,252,320G/Cuncertain significance
rs75227931:171,252,442T/A
rs7502796401:171,254,381A/Tuncertain significance
rs13308378631:171,254,409A/Guncertain significance
rs7725202251:171,254,438A/Guncertain significance
rs13966786461:171,254,466T/Cuncertain significance
rs1402526801:171,254,504C/Tuncertain significance
rs5546390941:171,254,565G/Auncertain significance
rs7473023781:171,254,643T/Guncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.