FRMPD2

FERM and PDZ domain containing 2

Summary

This gene encodes a peripheral membrane protein and is located in a region of chromosome 10q that contains a segmental duplication. This copy of the gene is full-length and is in the telomeric duplicated region. Two other more centromerically proximal copies of the gene are partial and may represent pseudogenes. This full-length gene appears to function in the establishment and maintenance of cell polarization. The protein is recruited to cell-cell junctions in an E-cadherin-dependent manner, and is selectively localized at the basolateral membrane in polarized epithelial cells. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Dec 2009]

Known Variants91 total

rsidPosition (GRCh37)AllelesClassClinVar
rs130835002510:49,365,385G/Auncertain significance
rs7795843310:49,371,043T/Cintron variant
rs78280940910:49,371,383A/Clikely benign
rs119053708410:49,371,509G/Auncertain significance
rs249334922410:49,371,585G/Auncertain significance
rs183800687510:49,371,593C/Auncertain significance
rs78249042810:49,371,617C/Tuncertain significance
rs249334952410:49,371,651G/Tuncertain significance
rs20120582110:49,371,664G/Alikely benign
rs142156496110:49,379,090C/Tuncertain significance
rs116447463410:49,379,111C/Tuncertain significance
rs146405592110:49,379,128G/Auncertain significance
rs6184002410:49,379,964T/C
rs37678088510:49,381,012G/Auncertain significance
rs78223251110:49,382,962C/Tuncertain significance
rs131052704210:49,383,934T/Guncertain significance
rs78248455410:49,386,107G/Tuncertain significance
rs78254071910:49,386,116C/Auncertain significance
rs15058163610:49,386,151G/Abenign
rs139186744410:49,386,179A/Cuncertain significance
rs20078352410:49,386,184G/Tlikely benign
rs125126008010:49,388,985T/Cuncertain significance
rs78240206910:49,389,045C/Tuncertain significance
rs140361352510:49,392,653T/Cuncertain significance
rs74562466310:49,392,662C/Tuncertain significance
rs14430189910:49,392,715T/Cuncertain significance
rs14630473710:49,392,852C/Guncertain significance
rs77403646310:49,392,886C/Guncertain significance
rs52900815910:49,392,912T/Cuncertain significance
rs37306054410:49,393,631C/Tlikely benign
rs76893526210:49,393,632G/Alikely benign
rs14172251610:49,393,643C/Tlikely benign
rs20043540710:49,393,649G/Auncertain significance
rs11424338910:49,395,237G/Cuncertain significance
rs7487851610:49,400,746C/Tbenign
rs97375123310:49,400,758T/Cuncertain significance
rs249343652410:49,400,774G/Tuncertain significance
rs249343698510:49,400,872T/Cuncertain significance
rs75019697210:49,400,901G/Alikely benign
rs96624278210:49,400,910T/Cuncertain significance
rs54293062210:49,406,110G/C
rs390661710:49,412,661C/Tintron variant
rs1110126310:49,414,181C/Tintron variant
rs53770687810:49,414,828C/Tuncertain significance
rs19976678710:49,414,876C/Tuncertain significance
rs142681577410:49,414,916T/Cuncertain significance
rs121807233510:49,414,942A/Tuncertain significance
rs249348239310:49,414,970G/Cuncertain significance
rs36800866510:49,420,077G/Auncertain significance
rs77761621410:49,420,106G/Tuncertain significance
rs14515247410:49,420,126G/Alikely benign
rs122712128610:49,430,025A/G
rs75955359810:49,430,369T/Clikely benign
rs249353958210:49,430,408A/Guncertain significance
rs74969793510:49,430,450T/Cuncertain significance
rs77309491510:49,430,477T/Auncertain significance
rs14451501410:49,430,493G/Tuncertain significance
rs74702074110:49,431,202C/Tuncertain significance
rs99879743410:49,431,227T/Cuncertain significance
rs249357126110:49,440,175C/Tuncertain significance
rs77663547010:49,440,181T/Guncertain significance
rs156443338610:49,440,236C/Auncertain significance
rs11614348010:49,440,275C/Tlikely benign
rs56195769210:49,444,538G/Auncertain significance
rs77445504810:49,444,550G/Auncertain significance
rs11639234310:49,444,555C/Tlikely benign
rs14350222310:49,446,060T/Glikely benign
rs20008251710:49,446,062T/Cuncertain significance
rs77238610010:49,446,085G/Tuncertain significance
rs54271456110:49,446,110C/Tuncertain significance
rs76283511510:49,446,166G/Tlikely benign
rs75892363710:49,447,663C/Tuncertain significance
rs78118358010:49,447,673T/Cuncertain significance
rs5580213610:49,447,720G/Alikely benign
rs20186547810:49,448,426G/Alikely benign
rs122695720910:49,448,429G/Auncertain significance
rs123653118210:49,448,446C/Guncertain significance
rs37771833310:49,448,462C/Tlikely benign
rs75875685910:49,450,223A/Guncertain significance
rs55392722310:49,450,245T/Guncertain significance
rs75000127810:49,450,275A/Tuncertain significance
rs77078485410:49,452,858C/Auncertain significance
rs74586555410:49,452,867G/Tuncertain significance
rs76035365610:49,452,882T/Cuncertain significance
rs76579393510:49,457,101T/Cuncertain significance
rs20155567010:49,457,150G/Cuncertain significance
rs7279225110:49,457,208A/Glikely benign
rs14333090510:49,457,215G/Auncertain significance
rs15022306410:49,459,615G/Auncertain significance
rs75267517110:49,459,666C/Tuncertain significance
rs37312912710:49,482,603G/Auncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.