GHSR

growth hormone secretagogue receptor

Summary

This gene encodes a member of the G-protein coupled receptor family. The encoded protein may play a role in energy homeostasis and regulation of body weight. Two identified transcript variants are expressed in several tissues and are evolutionary conserved in fish and swine. One transcript, 1a, excises an intron and encodes the functional protein; this protein is the receptor for the Ghrelin ligand and defines a neuroendocrine pathway for growth hormone release. The second transcript (1b) retains the intron and does not function as a receptor for Ghrelin; however, it may function to attenuate activity of isoform 1a. Mutations in this gene are associated with autosomal idiopathic short stature.[provided by RefSeq, Apr 2010]

Known Variants200 total

rsidPosition (GRCh37)AllelesClassClinVar
rs5425287483:172,161,094C/Tuncertain significance
rs8860581783:172,161,119C/Tuncertain significance
rs7626042093:172,161,136G/Cuncertain significance
rs10273808603:172,161,146C/Tuncertain significance
rs1901455193:172,161,176C/Tlikely benign
rs284767223:172,161,215T/Cbenign
rs1150011883:172,161,223T/Clikely benign
rs5446105713:172,161,239A/Tuncertain significance
rs8860581793:172,161,343G/Auncertain significance
rs7543521553:172,161,397G/Auncertain significance
rs17373908523:172,161,419G/Cuncertain significance
rs8860581803:172,161,445G/Tuncertain significance
rs8972650753:172,161,506T/Cuncertain significance
rs8860581813:172,161,606C/Auncertain significance
rs730390283:172,161,643A/Cbenign
rs7559253353:172,161,683A/Guncertain significance
rs1398445243:172,161,790G/Alikely benign
rs1827325623:172,161,793C/Tlikely benign
rs5624163:172,161,842C/Abenign
rs13705443333:172,161,878T/Cuncertain significance
rs7567286403:172,161,905A/Tuncertain significance
rs98802063:172,161,927C/Gbenign
rs10485849053:172,162,001T/Guncertain significance
rs8860581823:172,162,109A/Tuncertain significance
rs5555794613:172,162,111T/Cuncertain significance
rs5651053:172,162,117G/Tbenign
rs5351104773:172,162,122G/Tlikely benign
rs1476836853:172,162,138T/Clikely benign
rs585509303:172,162,155T/Abenign
rs98806523:172,162,159C/Gbenign
rs8860581833:172,162,193C/Tuncertain significance
rs17374112723:172,162,204C/Auncertain significance
rs17374126403:172,162,275G/Auncertain significance
rs9342784463:172,162,439T/Cuncertain significance
rs8860581843:172,162,479G/Auncertain significance
rs1397787593:172,162,553G/Alikely benign
rs1838707763:172,162,573A/Glikely benign
rs8860581853:172,162,651C/Tuncertain significance
rs5439208673:172,162,657G/Tuncertain significance
rs4822043:172,162,829A/Gbenign
rs4772513:172,162,837T/Cbenign
rs17374277193:172,162,946C/Tuncertain significance
rs7612388263:172,162,964C/Tuncertain significance
rs21084247423:172,162,966A/Tlikely benign
rs1503441133:172,162,980C/Tconflicting classifications of pathogenicity
rs2021129063:172,162,982C/Tconflicting classifications of pathogenicity
rs7506038633:172,162,983G/Auncertain significance
rs1380636483:172,162,987A/Tuncertain significance
rs7770166253:172,163,001G/Auncertain significance
rs2006330783:172,163,003G/Cuncertain significance
rs21084247843:172,163,010G/Auncertain significance
rs730390313:172,163,023G/Alikely benign
rs1447204273:172,163,032G/Alikely benign
rs1385078143:172,163,035T/Cconflicting classifications of pathogenicity
rs24735542473:172,163,038C/Tlikely benign
rs17374311513:172,163,054G/Auncertain significance
rs2019438623:172,163,058C/Guncertain significance
rs2011625573:172,163,061G/Auncertain significance
rs3747819433:172,163,074C/Tuncertain significance
rs1492495223:172,163,078A/Tuncertain significance
rs7580196643:172,163,080G/Alikely benign
rs8687281523:172,163,093G/Tuncertain significance
rs24735544463:172,163,112G/Auncertain significance
rs1455608013:172,163,128G/Cconflicting classifications of pathogenicity
rs17374336993:172,163,158A/Glikely benign
rs12197478363:172,163,178G/Auncertain significance
rs7503785613:172,163,186G/Auncertain significance
rs1483712133:172,163,205G/Auncertain significance
rs24735546033:172,163,220G/Tuncertain significance
rs14388538503:172,163,221G/Alikely benign
rs7477111563:172,163,223G/Auncertain significance
rs7694529623:172,163,228C/Guncertain significance
rs1995999953:172,163,229A/Gconflicting classifications of pathogenicity
rs7711468683:172,163,232G/Auncertain significance
rs9764860973:172,163,233G/Alikely benign
rs1415960223:172,163,235T/Clikely benign
rs2015498763:172,163,236G/Alikely benign
rs3684920403:172,163,252A/Guncertain significance
rs24735547373:172,163,264A/Tuncertain significance
rs5090353:172,163,449G/Aintron variantbenign
rs29486943:172,165,163A/Gintron variantbenign
rs1999967283:172,165,390G/Alikely benign
rs7804096813:172,165,394G/Alikely benign
rs7697970703:172,165,412C/Tuncertain significance
rs11630686213:172,165,425T/Guncertain significance
rs1401349273:172,165,427C/Auncertain significance
rs24735569253:172,165,431T/Cuncertain significance
rs2002803293:172,165,432G/Auncertain significance
rs2003676963:172,165,449G/Auncertain significance
rs7593567633:172,165,459C/Auncertain significance
rs11881500903:172,165,467T/Guncertain significance
rs11765540553:172,165,471C/Tuncertain significance
rs7483240673:172,165,491T/Cuncertain significance
rs7777772483:172,165,494C/Tuncertain significance
rs1995889043:172,165,495T/Amissense variantuncertain significance
rs24735570573:172,165,500A/Guncertain significance
rs7721784003:172,165,501T/Cuncertain significance
rs3756987693:172,165,502G/Alikely benign
rs2008049103:172,165,518G/Auncertain significance
rs21084262013:172,165,534G/Cuncertain significance

Showing 100 of 200 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.