GTF2H1

general transcription factor IIH subunit 1

Summary

Enables nuclear thyroid hormone receptor binding activity. Involved in positive regulation of DNA-templated transcription and transcription initiation at RNA polymerase II promoter. Located in nucleoplasm. Part of transcription factor TFIIH core complex and transcription factor TFIIH holo complex. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants35 total

rsidPosition (GRCh37)AllelesClassClinVar
rs415054211:18,345,848G/Aupstream gene variant
rs1102462211:18,352,685C/A
rs78137514211:18,354,754C/Tuncertain significance
rs55195926311:18,355,124T/C
rs415058111:18,357,270A/Gintron variant
rs76647597611:18,357,365C/Auncertain significance
rs76785595811:18,357,369A/Guncertain significance
rs75760731311:18,357,388A/Guncertain significance
rs186501401311:18,357,391A/Guncertain significance
rs146465894611:18,357,394G/Auncertain significance
rs15127334311:18,357,419A/Gbenign
rs186507882911:18,359,798G/Cuncertain significance
rs7788595911:18,362,382T/Gintron variant
rs37236880311:18,362,901G/Auncertain significance
rs186515217711:18,362,938T/Guncertain significance
rs249448745511:18,363,134G/Auncertain significance
rs249448747411:18,363,143C/Auncertain significance
rs14469057611:18,369,135G/Auncertain significance
rs77891995911:18,369,196A/Guncertain significance
rs14329350611:18,369,438C/Guncertain significance
rs415064211:18,370,898G/A
rs77350351911:18,373,482A/Cuncertain significance
rs141143167811:18,373,486C/Tuncertain significance
rs167380659911:18,373,515A/Guncertain significance
rs249452234711:18,373,933T/Guncertain significance
rs75791996611:18,373,971C/Tuncertain significance
rs37326263611:18,379,553G/Tuncertain significance
rs142107484311:18,379,554C/Tuncertain significance
rs186560315111:18,379,571A/Guncertain significance
rs13896512311:18,380,094A/Cuncertain significance
rs36931001711:18,382,231C/Tuncertain significance
rs75022425311:18,382,239G/Cuncertain significance
rs415067811:18,384,170C/Gintron variant
rs978334711:18,384,938A/C
rs6175464611:18,387,342G/Alikely benign

Gene information from NCBI Gene. Variant classifications from ClinVar.