HEY2

hes related family bHLH transcription factor with YRPW motif 2

Summary

This gene encodes a member of the hairy and enhancer of split-related (HESR) family of basic helix-loop-helix (bHLH)-type transcription factors. The encoded protein forms homo- or hetero-dimers that localize to the nucleus and interact with a histone deacetylase complex to repress transcription. Expression of this gene is induced by the Notch signal transduction pathway. Two similar and redundant genes in mouse are required for embryonic cardiovascular development, and are also implicated in neurogenesis and somitogenesis. Alternatively spliced transcript variants have been found, but their biological validity has not been determined. [provided by RefSeq, Jul 2008]

Known Variants30 total

rsidPosition (GRCh37)AllelesClassClinVar
rs37572176:126,069,636G/T
rs77640166:126,070,789T/A
rs24826631646:126,070,927A/Tuncertain significance
rs9349594186:126,070,935T/Auncertain significance
rs7549156746:126,070,951C/Tuncertain significance
rs1384722616:126,070,962A/Guncertain significance
rs14765210266:126,070,977G/Auncertain significance
rs18118526:126,071,575G/Cupstream gene variant
rs7488543466:126,072,960T/Cuncertain significance
rs1930353946:126,073,140T/Cbenign
rs1122359076:126,073,212T/Gbenign
rs1483043016:126,073,225T/Cuncertain significance
rs1126777236:126,073,244A/Tbenign
rs13197991706:126,075,687G/Auncertain significance
rs17737297986:126,080,388C/Tuncertain significance
rs7780060426:126,080,414C/Guncertain significance
rs7719624306:126,080,448T/Cuncertain significance
rs1400103446:126,080,470C/Tuncertain significance
rs3771491076:126,080,481C/Tuncertain significance
rs9964722006:126,080,556A/Tuncertain significance
rs24826847626:126,080,605C/Tuncertain significance
rs12470316546:126,080,634G/Cuncertain significance
rs17737461816:126,080,665G/Cuncertain significance
rs24826855546:126,080,806C/Auncertain significance
rs3742772366:126,080,808A/Guncertain significance
rs1457521736:126,080,823G/Alikely benign
rs7485488296:126,080,848C/Tuncertain significance
rs1389662786:126,080,899C/Auncertain significance
rs9274276696:126,080,919C/Tuncertain significance
rs37346376:126,081,319G/T3 prime UTR variant

Gene information from NCBI Gene. Variant classifications from ClinVar.