IQSEC1

IQ motif and Sec7 domain ArfGEF 1

Summary

Predicted to enable protein kinase binding activity. Predicted to be involved in several processes, including positive regulation of focal adhesion disassembly; positive regulation of keratinocyte migration; and regulation of postsynaptic neurotransmitter receptor internalization. Located in centrosome; cytosol; and nucleoplasm. Implicated in intellectual developmental disorder with short stature and behavioral abnormalities and lung adenocarcinoma. Biomarker of lung non-small cell carcinoma. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants153 total

rsidPosition (GRCh37)AllelesClassClinVar
rs8972024133:12,942,501C/Auncertain significance
rs1995242433:12,942,577C/Tbenign
rs24701960523:12,942,583C/Tuncertain significance
rs14859962353:12,942,588G/Auncertain significance
rs5618428693:12,942,594G/Auncertain significance
rs24701969323:12,942,603C/Tuncertain significance
rs5594597113:12,942,625C/Tlikely benign
rs24702013253:12,942,684G/Auncertain significance
rs24702020783:12,942,694G/Auncertain significance
rs24702022343:12,942,697G/Auncertain significance
rs731413603:12,942,710C/Tbenign
rs3755835113:12,942,749C/Tlikely benign
rs5346794163:12,942,758G/Alikely benign
rs1851650593:12,942,760C/Gbenign
rs5714263723:12,942,761G/Alikely benign
rs5738687643:12,942,788C/Tbenign
rs24702057123:12,942,798C/Tuncertain significance
rs7717243853:12,942,799C/Tuncertain significance
rs24702072153:12,942,843G/Auncertain significance
rs7639187263:12,942,844G/Auncertain significance
rs8668191283:12,942,848T/Glikely benign
rs24702079243:12,942,858T/Glikely benign
rs5310612353:12,942,939G/Alikely benign
rs9514219533:12,942,970T/Auncertain significance
rs14556830123:12,942,992G/Auncertain significance
rs11666598463:12,942,994C/Tuncertain significance
rs1908096783:12,943,013T/Glikely benign
rs7469436833:12,943,018G/Auncertain significance
rs1396032213:12,944,298G/Auncertain significance
rs16945118033:12,944,314C/Tlikely benign
rs26003243:12,945,271A/T
rs7618278443:12,949,857G/Auncertain significance
rs5604245563:12,949,867G/Auncertain significance
rs16952136593:12,949,878C/Tuncertain significance
rs7511394673:12,949,906C/Tuncertain significance
rs7508544783:12,949,962T/Cuncertain significance
rs5627007353:12,949,999C/Tuncertain significance
rs175414053:12,950,002C/Tlikely benign
rs11735281313:12,950,832G/Auncertain significance
rs3690924363:12,950,842T/Guncertain significance
rs7761551903:12,950,856T/Cuncertain significance
rs7646838033:12,950,864G/Alikely benign
rs15758723443:12,953,133G/Tuncertain significance
rs1466682703:12,953,139G/Cuncertain significance
rs7775165983:12,953,191G/Auncertain significance
rs7764670623:12,954,972C/Tuncertain significance
rs7519765253:12,955,050G/Auncertain significance
rs25969023:12,955,982G/Aintron variant
rs16959497913:12,956,599C/Tuncertain significance
rs2001694903:12,957,095G/Auncertain significance
rs24705399033:12,957,159T/Cuncertain significance
rs13879079713:12,957,165C/Guncertain significance
rs2022072353:12,957,167C/Auncertain significance
rs1999553953:12,957,173C/Auncertain significance
rs1411639633:12,957,174G/Tuncertain significance
rs7621886443:12,957,180G/Cuncertain significance
rs24705409663:12,957,195T/Guncertain significance
rs3685963723:12,961,941T/Cuncertain significance
rs1461071473:12,961,967C/Glikely benign
rs7682630523:12,962,046G/Auncertain significance
rs7666385383:12,962,047G/Cuncertain significance
rs7542354733:12,962,052C/Tuncertain significance
rs7630337323:12,962,063C/Tlikely benign
rs24706891433:12,963,627C/Auncertain significance
rs7760679683:12,963,673G/Alikely benign
rs1999990913:12,963,730G/Alikely benign
rs7534111853:12,966,089G/Alikely benign
rs9003906063:12,966,100A/Cuncertain significance
rs12054414723:12,966,127C/Tuncertain significance
rs622426703:12,967,889G/Aintron variant
rs7674402683:12,976,968G/Alikely benign
rs1512924543:12,976,989G/Alikely benign
rs37326853:12,977,088C/Tlikely benign
rs16981011133:12,977,135T/Cuncertain significance
rs1410425523:12,977,185T/Guncertain significance
rs1447903333:12,977,230C/Tlikely benign
rs7566002133:12,977,239C/Tuncertain significance
rs1429228983:12,977,245C/Tuncertain significance
rs5351137233:12,977,246G/Auncertain significance
rs24709574003:12,977,280G/Alikely benign
rs7467169113:12,977,285C/Tuncertain significance
rs1503865853:12,977,335T/Cuncertain significance
rs1490929043:12,977,370C/Tlikely benign
rs8663077303:12,977,374C/Tuncertain significance
rs7546066593:12,977,375G/Auncertain significance
rs7642773113:12,977,438C/Tuncertain significance
rs1484270423:12,977,451C/Guncertain significance
rs7456158243:12,977,470G/Auncertain significance
rs7657236073:12,977,488G/Apathogenic
rs7738843763:12,977,493C/Glikely benign
rs3722288873:12,977,543C/Tconflicting classifications of pathogenicity
rs7581705223:12,977,554C/Tlikely pathogenic
rs7471958583:12,977,555G/Auncertain significance
rs7482150133:12,977,560C/Guncertain significance
rs16981618963:12,977,567C/Auncertain significance
rs1432226513:12,977,574G/Alikely benign
rs10215963653:12,977,575G/Cuncertain significance
rs7598315913:12,977,576T/Cuncertain significance
rs5447765003:12,977,583C/Tlikely benign
rs5615712113:12,977,584G/Auncertain significance

Showing 100 of 153 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.