KIFAP3

kinesin associated protein 3

Summary

The small G protein GDP dissociation stimulator (smg GDS) is a regulator protein having two activities on a group of small G proteins including the Rho and Rap1 family members and Ki-Ras; one is to stimulate their GDP/GTP exchange reactions, and the other is to inhibit their interactions with membranes. The protein encoded by this gene contains 9 'Armadillo' repeats and interacts with the smg GDS protein through these repeats. This protein, which is highly concentrated around the endoplasmic reticulum, is phosphorylated by v-src, and this phosphorylation reduces the affinity of the protein for smg GDS. It is thought that this protein serves as a linker between human chromosome-associated polypeptide (HCAP) and KIF3A/B, a kinesin superfamily protein in the nucleus, and that it plays a role in the interaction of chromosomes with an ATPase motor protein. Several transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Mar 2011]

Known Variants32 total

rsidPosition (GRCh37)AllelesClassClinVar
rs7535761671:169,890,863T/Guncertain significance
rs2011571591:169,923,170T/Cuncertain significance
rs7514284691:169,923,211G/Tuncertain significance
rs25269518231:169,923,224A/Guncertain significance
rs5080631:169,923,676A/C
rs7795662271:169,930,235T/Cuncertain significance
rs1497947211:169,938,684C/Tintron variant
rs7743714861:169,947,244C/Tuncertain significance
rs1132998871:169,950,203T/Cintron variant
rs413021211:169,951,117T/Clikely benign
rs12414362251:169,951,920G/Tuncertain significance
rs13227226151:169,951,966C/Tuncertain significance
rs120758331:169,951,978A/Cbenign
rs7489756581:169,953,745T/Guncertain significance
rs1167559241:169,953,815A/Cbenign
rs1490275441:169,961,335G/Abenign
rs25271683161:169,961,345A/Cuncertain significance
rs25273207401:169,985,659C/Tuncertain significance
rs25273207871:169,985,666C/Guncertain significance
rs25273712591:169,993,648C/Tuncertain significance
rs25273717691:169,993,704T/Cuncertain significance
rs15411601:169,995,802C/G
rs360226481:170,001,034T/Cbenign
rs7802116241:170,008,394G/Auncertain significance
rs10192095581:170,010,879A/Glikely benign
rs5374075351:170,010,897C/Tlikely benign
rs2014414721:170,015,873C/Tuncertain significance
rs741223081:170,015,915A/Cuncertain significance
rs13176549611:170,015,970T/Cuncertain significance
rs25275569241:170,024,563C/Tuncertain significance
rs11876093781:170,043,604T/Auncertain significance
rs5224441:170,043,904G/T

Gene information from NCBI Gene. Variant classifications from ClinVar.