LMO1

LIM domain only 1

Summary

This locus encodes a transcriptional regulator that contains two cysteine-rich LIM domains but lacks a DNA-binding domain. LIM domains may play a role in protein interactions; thus the encoded protein may regulate transcription by competitively binding to specific DNA-binding transcription factors. Alterations at this locus have been associated with acute lymphoblastic T-cell leukemia. Chromosomal rearrangements have been observed between this locus and at least two loci, the delta subunit of the T-cell antigen receptor gene and the LIM domain binding 1 gene. Alternatively spliced transcript variants have been described. [provided by RefSeq, Jul 2012]

Known Variants15 total

rsidPosition (GRCh37)AllelesClassClinVar
rs121324831011:8,246,185G/Auncertain significance
rs213450521611:8,246,249A/Tuncertain significance
rs795232011:8,250,143G/Cintron variant
rs475831711:8,250,811C/Aregulatory region variant
rs77647376511:8,251,899C/Tuncertain significance
rs37394850111:8,251,959A/Cuncertain significance
rs78050267611:8,252,031G/Tuncertain significance
rs11041911:8,252,853A/Gintron variant
rs216810111:8,255,408C/Aregulatory region variantbenign
rs44226411:8,264,149G/T
rs48416111:8,264,525T/G
rs53395776911:8,264,987A/C
rs379401211:8,270,244T/Cintron variant
rs423777011:8,275,835T/G
rs1104182911:8,276,735A/Tintron variant

Gene information from NCBI Gene. Variant classifications from ClinVar.