MGAT3

beta-1,4-mannosyl-glycoprotein 4-beta-N-acetylglucosaminyltransferase

Summary

There are believed to be over 100 different glycosyltransferases involved in the synthesis of protein-bound and lipid-bound oligosaccharides. The enzyme encoded by this gene transfers a GlcNAc residue to the beta-linked mannose of the trimannosyl core of N-linked oligosaccharides and produces a bisecting GlcNAc. Multiple alternatively spliced variants, encoding the same protein, have been identified. [provided by RefSeq, Jul 2008]

Known Variants31 total

rsidPosition (GRCh37)AllelesClassClinVar
rs11320047322:39,853,740G/Aregulatory region variant
rs200698722:39,855,082T/C
rs90967422:39,859,169C/G
rs728691722:39,860,868A/Gintron variant
rs76071322:39,875,595G/Cupstream gene variant
rs102313738422:39,883,365C/Guncertain significance
rs77584815822:39,883,383A/Guncertain significance
rs251797639722:39,883,482A/Cuncertain significance
rs14579100622:39,883,564G/Auncertain significance
rs20072661922:39,883,576A/Guncertain significance
rs97960367422:39,883,797C/Auncertain significance
rs77629974822:39,883,800C/Guncertain significance
rs76264851922:39,883,815G/Alikely benign
rs75493165522:39,883,828C/Guncertain significance
rs36893230822:39,883,878G/Auncertain significance
rs128125117922:39,883,912T/Auncertain significance
rs20191694222:39,883,927A/Cuncertain significance
rs55825005822:39,883,974G/Auncertain significance
rs128746275422:39,884,117G/Cuncertain significance
rs75301599822:39,884,274C/Guncertain significance
rs13981269222:39,884,279C/Tbenign
rs14250449422:39,884,357C/Gbenign
rs214572875022:39,884,466G/Alikely benign
rs37117272922:39,884,531A/Cuncertain significance
rs251797876422:39,884,667G/Alikely benign
rs14133353722:39,884,765G/Cuncertain significance
rs14831942922:39,884,826G/Cuncertain significance
rs120725700622:39,884,892C/Tuncertain significance
rs76943158722:39,884,919C/Tuncertain significance
rs76615034522:39,884,929G/Auncertain significance
rs75155110522:39,884,940G/Auncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.