NDUFB1

NADH:ubiquinone oxidoreductase subunit B1

Summary

Predicted to enable NADH dehydrogenase (ubiquinone) activity. Predicted to be involved in mitochondrial electron transport, NADH to ubiquinone and proton motive force-driven mitochondrial ATP synthesis. Located in mitochondrial inner membrane and nuclear speck. Part of respiratory chain complex I. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants7 total

rsidPosition (GRCh37)AllelesClassClinVar
rs1116004414:92,582,655T/C
rs125199395014:92,583,837C/Tnot provided
rs14547311014:92,583,866C/Guncertain significance
rs128866119514:92,587,991G/Auncertain significance
rs36991452014:92,588,016G/Auncertain significance
rs20092863814:92,588,106G/Auncertain significance
rs56976020014:92,588,531C/T

Gene information from NCBI Gene. Variant classifications from ClinVar.