NMT1

N-myristoyltransferase 1

Summary

Myristate, a rare 14-carbon saturated fatty acid, is cotranslationally attached by an amide linkage to the N-terminal glycine residue of cellular and viral proteins with diverse functions. N-myristoyltransferase (NMT; EC 2.3.1.97) catalyzes the transfer of myristate from CoA to proteins. N-myristoylation appears to be irreversible and is required for full expression of the biologic activities of several N-myristoylated proteins, including the alpha subunit of the signal-transducing guanine nucleotide-binding protein (G protein) GO (GNAO1; MIM 139311) (Duronio et al., 1992 [PubMed 1570339]).[supplied by OMIM, Nov 2008]

Known Variants19 total

rsidPosition (GRCh37)AllelesClassClinVar
rs7728888817:43,143,662A/Gintron variant
rs650341717:43,144,218T/Cupstream gene variant
rs479316917:43,152,877T/G
rs5636093517:43,156,135A/Tintron variant
rs721426717:43,157,709G/T
rs121252273117:43,159,023C/Tuncertain significance
rs205401826717:43,159,098C/Tuncertain significance
rs128161479017:43,159,109C/Auncertain significance
rs86871843617:43,163,951G/Tuncertain significance
rs15041875317:43,174,504G/Auncertain significance
rs37621805817:43,175,907G/Auncertain significance
rs1293623417:43,177,951T/Cintron variant
rs75033067817:43,180,320C/Guncertain significance
rs76013833017:43,180,331G/Auncertain significance
rs214352345417:43,180,386C/Guncertain significance
rs120809920117:43,180,413C/Tuncertain significance
rs14848386817:43,180,418G/Auncertain significance
rs77305295517:43,181,117C/Tuncertain significance
rs77430189917:43,182,299A/Guncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.