NOA1

nitric oxide associated 1

Summary

The protein encoded by this gene is a nuclear-encoded GTPase that functions in the mitochondrion. Upon translation, this protein is imported into the nucleus and then into the nucleolus before being exported to the mitochondrion. The encoded protein is required for oxygen-dependent regulation of mitochondrial respiratory complexes and for mitochondrial protein synthesis. [provided by RefSeq, Dec 2015]

Known Variants53 total

rsidPosition (GRCh37)AllelesClassClinVar
rs3735949834:57,829,651T/Cuncertain significance
rs24758881164:57,829,652G/Alikely benign
rs2012632844:57,829,656A/Guncertain significance
rs7471115114:57,829,683T/Cuncertain significance
rs7729476414:57,829,719T/Auncertain significance
rs7812825814:57,829,750C/Tuncertain significance
rs24758884744:57,829,766T/Auncertain significance
rs7784927424:57,830,589A/Tuncertain significance
rs10150098864:57,830,596C/Guncertain significance
rs3748976164:57,830,667A/Guncertain significance
rs7817536314:57,832,824C/Tlikely benign
rs1483407814:57,832,831C/Tlikely benign
rs3698479424:57,832,843G/Clikely benign
rs5322162664:57,832,875C/Tuncertain significance
rs9745232224:57,834,635G/Auncertain significance
rs355148524:57,835,969C/Tintron variant
rs726275094:57,839,051C/Gupstream gene variant
rs572652574:57,839,280A/Tupstream gene variant
rs7654649564:57,839,373G/Clikely benign
rs777972394:57,839,419A/Gbenign
rs7511866374:57,839,464A/Tuncertain significance
rs3708160164:57,840,027C/Tuncertain significance
rs3710385794:57,840,152T/Cuncertain significance
rs726064044:57,841,213G/A
rs17219244354:57,842,644C/Tuncertain significance
rs3745949444:57,842,667T/Guncertain significance
rs3687391814:57,842,806T/Cuncertain significance
rs7786653994:57,842,863C/Glikely benign
rs24759033954:57,842,874T/Auncertain significance
rs1481814994:57,842,895G/Auncertain significance
rs7787356754:57,842,929C/Guncertain significance
rs2007054214:57,842,943T/Cuncertain significance
rs2019988484:57,842,977C/Guncertain significance
rs5335551434:57,843,058G/Auncertain significance
rs9975304444:57,843,076G/Cuncertain significance
rs13758726254:57,843,115C/Guncertain significance
rs24759044254:57,843,147A/Guncertain significance
rs7777092874:57,843,167C/Auncertain significance
rs5643359954:57,843,175G/Auncertain significance
rs12654074904:57,843,210C/Guncertain significance
rs7469211214:57,843,220C/Guncertain significance
rs7707383144:57,843,222G/Cuncertain significance
rs7703849744:57,843,237C/Tuncertain significance
rs7518114304:57,843,296G/Tuncertain significance
rs7538277734:57,843,348G/Cuncertain significance
rs13188250534:57,843,382G/Auncertain significance
rs24759057534:57,843,411T/Guncertain significance
rs24759064464:57,843,528G/Cuncertain significance
rs3771436714:57,843,548C/Auncertain significance
rs13512104084:57,843,651C/Tuncertain significance
rs5295542834:57,843,658G/Cuncertain significance
rs2019576164:57,843,732G/Tbenign
rs7756306444:57,843,738C/Guncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.