NPLOC4

NPL4 homolog, ubiquitin recognition factor

Summary

Predicted to enable ubiquitin binding activity and ubiquitin protein ligase binding activity. Predicted to contribute to K48-linked polyubiquitin modification-dependent protein binding activity and K63-linked polyubiquitin modification-dependent protein binding activity. Involved in negative regulation of RIG-I signaling pathway; negative regulation of type I interferon production; and proteolysis involved in protein catabolic process. Located in nucleus. Part of UFD1-NPL4 complex and VCP-NPL4-UFD1 AAA ATPase complex. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants40 total

rsidPosition (GRCh37)AllelesClassClinVar
rs36949088517:79,526,315G/Cuncertain significance
rs11331871717:79,526,379G/Abenign
rs76075237617:79,526,401C/Tuncertain significance
rs76574984717:79,526,404C/Tuncertain significance
rs20162234017:79,526,422G/Clikely benign
rs20109508917:79,526,432G/Abenign
rs807092917:79,530,993G/Tregulatory region variant
rs254450633317:79,532,543C/Tuncertain significance
rs254451189417:79,534,501G/Auncertain significance
rs57818868317:79,536,062C/Tuncertain significance
rs116709098417:79,536,097G/Tuncertain significance
rs77990059517:79,536,114A/Cuncertain significance
rs1785230717:79,539,073C/Abenign
rs1294995617:79,542,813C/Tdownstream gene variant
rs3463536317:79,549,250G/C
rs1295322917:79,554,271G/Aintron variant
rs1294870817:79,558,741G/Aintron variant
rs254456892017:79,563,192A/Guncertain significance
rs1165612617:79,564,542G/Aintron variant
rs36822605017:79,571,711C/Tuncertain significance
rs92291663317:79,573,730G/Auncertain significance
rs76982198317:79,573,737C/Tuncertain significance
rs117131440217:79,575,837C/Guncertain significance
rs807703817:79,577,127T/C
rs37426981517:79,577,256C/Tuncertain significance
rs11236425417:79,578,287G/Aintron variant
rs37136032617:79,580,375C/Tuncertain significance
rs148076480217:79,580,426C/Tuncertain significance
rs20194832217:79,580,437T/Cuncertain significance
rs77609822617:79,580,446G/Alikely benign
rs750322117:79,583,371C/Aintron variant
rs750389417:79,583,473T/Cintron variant
rs7507829217:79,585,492A/C
rs76073574917:79,589,203C/Guncertain significance
rs75313423917:79,589,255T/Cuncertain significance
rs77819915917:79,589,259T/Guncertain significance
rs6158642517:79,590,835C/G
rs254464593817:79,596,788G/Auncertain significance
rs989442917:79,596,811C/Tsynonymous variant
rs990578617:79,602,063G/A

Gene information from NCBI Gene. Variant classifications from ClinVar.