NR1H2

nuclear receptor subfamily 1 group H member 2

Summary

The liver X receptors, LXRA (NR1H3; MIM 602423) and LXRB, form a subfamily of the nuclear receptor superfamily and are key regulators of macrophage function, controlling transcriptional programs involved in lipid homeostasis and inflammation. The inducible LXRA is highly expressed in liver, adrenal gland, intestine, adipose tissue, macrophages, lung, and kidney, whereas LXRB is ubiquitously expressed. Ligand-activated LXRs form obligate heterodimers with retinoid X receptors (RXRs; see MIM 180245) and regulate expression of target genes containing LXR response elements (summary by Korf et al., 2009 [PubMed 19436111]).[supplied by OMIM, Jan 2010]

Known Variants12 total

rsidPosition (GRCh37)AllelesClassClinVar
rs1737308019:50,879,524C/Gregulatory region variantbenign
rs5615114819:50,879,552C/Tregulatory region variant
rs269512119:50,880,741T/Cregulatory region variant
rs251384427519:50,880,996G/Auncertain significance
rs136649853519:50,881,023C/Tuncertain significance
rs100380548419:50,881,059G/Tuncertain significance
rs2851489419:50,881,326T/Cintron variantbenign
rs77768585219:50,881,436G/Tuncertain significance
rs224894919:50,882,169A/Gintron variant
rs140565519:50,882,619T/G
rs156859547719:50,883,059G/Auncertain significance
rs230304419:50,885,201C/Tupstream gene variant

Gene information from NCBI Gene. Variant classifications from ClinVar.