PKLR

pyruvate kinase L/R

Summary

The protein encoded by this gene is a pyruvate kinase that catalyzes the transphosphorylation of phohsphoenolpyruvate into pyruvate and ATP, which is the rate-limiting step of glycolysis. Defects in this enzyme, due to gene mutations or genetic variations, are the common cause of chronic hereditary nonspherocytic hemolytic anemia (CNSHA or HNSHA). Multiple transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Jul 2008]

Known Variants269 total

rsidPosition (GRCh37)AllelesClassClinVar
rs9172443001:155,259,086C/T—uncertain significance
rs9377951861:155,259,258C/T—uncertain significance
rs5598099161:155,259,296A/G—uncertain significance
rs5287405501:155,259,322G/A—uncertain significance
rs88471:155,259,323C/T—benign
rs412649391:155,259,470A/C—uncertain significance
rs8860453471:155,259,497A/G—uncertain significance
rs8860453481:155,259,584G/T—uncertain significance
rs16744551241:155,259,608A/G—uncertain significance
rs1809447191:155,259,628T/C—uncertain significance
rs7581390941:155,259,781C/T—uncertain significance
rs16744632811:155,259,863G/A—uncertain significance
rs7775735001:155,259,864C/T—uncertain significance
rs16744709801:155,260,007A/G—uncertain significance
rs8860453491:155,260,012A/T—uncertain significance
rs8790403551:155,260,021G/A—uncertain significance
rs8860453501:155,260,088G/A—uncertain significance
rs9329721:155,260,096G/A—benign
rs81779941:155,260,349G/A—conflicting classifications of pathogenicity
rs10521771:155,260,350A/C—uncertain significance
rs617554311:155,260,382C/T—uncertain significance
rs10521761:155,260,383G/A—conflicting classifications of pathogenicity
rs1408596411:155,260,402G/A—likely benign
rs14561589561:155,260,412C/G—likely pathogenic
rs5322303121:155,260,413G/C—likely pathogenic
rs16744890861:155,260,418C/G—conflicting classifications of pathogenicity
rs7736284301:155,260,433A/G—uncertain significance
rs3703164621:155,260,434C/T—uncertain significance
rs3755252111:155,260,448C/G—uncertain significance
rs7510504251:155,260,449G/A—uncertain significance
rs11693152161:155,260,465C/G—uncertain significance
rs7776099661:155,260,472G/T—uncertain significance
rs3743293291:155,260,475G/A—likely benign
rs3772544621:155,261,532G/T—likely benign
rs9833945961:155,261,545A/G—pathogenic
rs9086901721:155,261,546C/T—likely pathogenic
rs2012170641:155,261,551T/A—conflicting classifications of pathogenicity
rs15720518951:155,261,558C/A—uncertain significance
rs16745532111:155,261,562A/G—uncertain significance
rs7582782001:155,261,570C/G—likely pathogenic
rs2012550241:155,261,571G/A—pathogenic
rs16745540411:155,261,574G/T—likely pathogenic
rs21481988971:155,261,590C/T—uncertain significance
rs5623181371:155,261,607G/T—uncertain significance
rs16745553271:155,261,610C/T—uncertain significance
rs7712183261:155,261,612C/T—uncertain significance
rs1390026291:155,261,613G/T—conflicting classifications of pathogenicity
rs1134038721:155,261,636C/Tmissense variantpathogenic
rs13317426331:155,261,637G/A—pathogenic
rs3760651161:155,261,647G/A—likely benign
rs81779881:155,261,649C/T—conflicting classifications of pathogenicity
rs1857537091:155,261,654C/T—likely pathogenic
rs9670102431:155,261,655G/A—conflicting classifications of pathogenicity
rs7502554011:155,261,657G/A—uncertain significance
rs7583277041:155,261,672C/T—conflicting classifications of pathogenicity
rs5518832181:155,261,673G/A—likely pathogenic
rs1415605321:155,261,681G/A—pathogenic
rs25252705001:155,261,682C/T—likely pathogenic
rs7462575861:155,261,696C/T—uncertain significance
rs2001330001:155,261,697G/A—uncertain significance
rs3691831991:155,261,702C/T—conflicting classifications of pathogenicity
rs9029886371:155,261,703G/A—pathogenic
rs7682108091:155,261,708C/T—uncertain significance
rs1161006951:155,261,709G/Amissense variantpathogenic
rs7730407381:155,261,723G/A—uncertain significance
rs37622721:155,261,777C/Tdownstream gene variantbenign
rs25252776011:155,262,966A/G—likely pathogenic
rs1182040851:155,262,968C/Amissense variantuncertain significance
rs2014067121:155,262,969G/A—conflicting classifications of pathogenicity
rs7742621101:155,262,970G/A—uncertain significance
rs25252778461:155,262,993T/A—likely pathogenic
rs16473215231:155,263,016G/A—uncertain significance
rs1499462711:155,263,025A/G—conflicting classifications of pathogenicity
rs7520349601:155,263,026C/T—conflicting classifications of pathogenicity
rs7555223961:155,263,031C/T—conflicting classifications of pathogenicity
rs1467087021:155,263,039G/A—conflicting classifications of pathogenicity
rs1893602831:155,263,059G/A—uncertain significance
rs13268954701:155,263,077G/A—uncertain significance
rs7711455761:155,263,086C/A—pathogenic
rs1422382681:155,263,101G/A—uncertain significance
rs25252795071:155,263,105G/T—pathogenic
rs7625913221:155,263,113C/T—uncertain significance
rs7680024931:155,263,127C/T—conflicting classifications of pathogenicity
rs16473386881:155,263,132A/C—uncertain significance
rs16473389521:155,263,137G/T—uncertain significance
rs7679813681:155,263,139A/C—conflicting classifications of pathogenicity
rs7771459751:155,263,141G/A—uncertain significance
rs16473396801:155,263,145C/T—uncertain significance
rs7784871091:155,263,149A/C—uncertain significance
rs21482021381:155,263,156T/A—uncertain significance
rs81779821:155,263,186A/G—conflicting classifications of pathogenicity
rs7746528171:155,263,229C/T—pathogenic
rs1182040841:155,263,237G/Tmissense variantpathogenic
rs7598555021:155,263,246C/T—uncertain significance
rs7565496121:155,263,248G/A—uncertain significance
rs16473464761:155,263,257G/C—likely pathogenic
rs7740063531:155,263,263T/G—uncertain significance
rs25252811381:155,263,264T/A—uncertain significance
rs8664729171:155,263,279C/T—pathogenic
rs7798179991:155,263,281C/T—uncertain significance

Showing 100 of 269 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.