PKNOX1

PBX/knotted 1 homeobox 1

Summary

Enables sequence-specific double-stranded DNA binding activity. Predicted to be involved in angiogenesis. Predicted to act upstream of or within camera-type eye development; hemopoiesis; and positive regulation of transcription by RNA polymerase II. Located in cytosol and nucleus. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants22 total

rsidPosition (GRCh37)AllelesClassClinVar
rs23475021:44,394,054C/T
rs812720921:44,423,282T/A
rs124318575521:44,424,523G/Auncertain significance
rs251729716521:44,430,245A/Tuncertain significance
rs75127175321:44,430,263G/Auncertain significance
rs283961821:44,433,454C/Gintron variant
rs283961921:44,436,177G/Aintron variant
rs75543210721:44,437,069C/Guncertain significance
rs19994424921:44,437,079C/Tuncertain significance
rs74611037221:44,438,320A/Guncertain significance
rs11142144721:44,439,332G/C
rs378804221:44,442,388G/Aintron variant
rs23472021:44,445,292C/Tintron variant
rs283962721:44,448,718C/Tintron variant
rs37768231721:44,448,909G/Auncertain significance
rs37638633021:44,448,954C/Auncertain significance
rs74931888821:44,448,968G/Tuncertain significance
rs76583623121:44,450,026G/Auncertain significance
rs76690531721:44,450,032A/Guncertain significance
rs75482905921:44,450,113G/Auncertain significance
rs129407401021:44,450,152G/Auncertain significance
rs37561970121:44,450,176G/Auncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.