PMVK

phosphomevalonate kinase

Summary

This gene encodes a peroxisomal enzyme that is a member of the galactokinase, homoserine kinase, mevalonate kinase, and phosphomevalonate kinase (GHMP) family of ATP-dependent enzymes. The encoded protein catalyzes the conversion of mevalonate 5-phosphate to mevalonate 5-diphosphate, which is the fifth step in the mevalonate pathway of isoprenoid biosynthesis. Mutations in this gene are linked to certain types of porokeratosis including disseminated superficial porokeratosis. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Feb 2017]

Known Variants29 total

rsidPosition (GRCh37)AllelesClassClinVar
rs7630781821:154,897,561A/Cbenign
rs3700675961:154,897,619G/Auncertain significance
rs7699710501:154,897,657C/Tuncertain significance
rs10479969671:154,897,734G/Tuncertain significance
rs3719133411:154,898,835G/Auncertain significance
rs13503467751:154,898,836T/Alikely benign
rs7459832071:154,898,860G/Astop gainedpathogenic
rs7799462721:154,898,874G/Auncertain significance
rs1512672861:154,898,881C/Guncertain significance
rs21019655981:154,898,893G/Alikely pathogenic
rs168365251:154,898,899C/Tbenign
rs1391454741:154,898,917G/Auncertain significance
rs1407287831:154,898,943C/Tlikely pathogenic
rs1823942631:154,899,755G/Aintron variant
rs1392488011:154,901,525A/Glikely benign
rs1485448511:154,901,589C/Guncertain significance
rs12101288401:154,901,632C/Auncertain significance
rs1149510741:154,903,917C/Tintron variant
rs18918051:154,904,840T/Cbenign
rs3753255791:154,904,883G/Cuncertain significance
rs75430511:154,905,179A/Gbenign
rs21019751131:154,908,901A/Guncertain significance
rs3730009761:154,909,083C/Apathogenic
rs412640431:154,909,131C/Tuncertain significance
rs173563611:154,909,169C/Tbenign
rs11098151:154,909,268A/Gbenign
rs586291291:154,910,930T/Cupstream gene variant
rs1911187921:154,910,978C/Tupstream gene variant
rs120464591:154,912,017A/Cupstream gene variant

Gene information from NCBI Gene. Variant classifications from ClinVar.