PPFIA2

PPFI scaffold protein A2

Summary

The protein encoded by this gene is a member of the LAR protein-tyrosine phosphatase-interacting protein (liprin) family. Liprins interact with members of LAR family of transmembrane protein tyrosine phosphatases, which are known to be important for axon guidance and mammary gland development. It has been proposed that liprins are multivalent proteins that form complex structures and act as scaffolds for the recruitment and anchoring of LAR family of tyrosine phosphatases. This protein has been shown to bind the calcium/calmodulin-dependent serine protein kinase (MAGUK family) protein (also known as CASK) and proposed to regulate higher-order brain functions in mammals. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Sep 2013]

Known Variants54 total

rsidPosition (GRCh37)AllelesClassClinVar
rs254122047112:81,657,048G/Tuncertain significance
rs36876439212:81,657,159T/Cuncertain significance
rs54818071512:81,660,772T/Cuncertain significance
rs203781216412:81,661,705T/Cuncertain significance
rs5624100812:81,661,822C/Tbenign
rs37389487612:81,671,124T/Guncertain significance
rs797181312:81,698,750A/C
rs192104512:81,714,932A/Gintron variant
rs36804764012:81,719,594G/Alikely benign
rs76328032612:81,719,598T/Cuncertain significance
rs74532813612:81,719,635T/Cuncertain significance
rs37718039212:81,732,973C/Tuncertain significance
rs254448434412:81,733,073C/Guncertain significance
rs18903296912:81,734,869T/Cuncertain significance
rs93829192412:81,734,983G/Tuncertain significance
rs37189086512:81,741,327C/Tuncertain significance
rs36903863212:81,741,332G/Auncertain significance
rs74701454412:81,741,379T/Cuncertain significance
rs37287985512:81,741,388G/Auncertain significance
rs3418736712:81,741,462A/Gbenign
rs75336771912:81,746,949G/Auncertain significance
rs36890997712:81,747,003G/Auncertain significance
rs37236151212:81,747,011G/Tuncertain significance
rs89456731312:81,747,055G/Cuncertain significance
rs206033483212:81,747,084G/Auncertain significance
rs143699626812:81,747,090T/Guncertain significance
rs76975033812:81,751,914C/Tuncertain significance
rs20123620612:81,751,967C/Tuncertain significance
rs52985167612:81,756,536G/Cuncertain significance
rs122380240612:81,756,547T/Cuncertain significance
rs76760161012:81,762,612A/Glikely benign
rs37742880812:81,762,942C/Tuncertain significance
rs18161999812:81,777,853A/Tuncertain significance
rs56802919612:81,777,857T/Clikely benign
rs254930095812:81,777,876C/Tuncertain significance
rs76230175612:81,777,896C/Tuncertain significance
rs203841798712:81,778,005T/Cuncertain significance
rs484239012:81,778,022C/Tuncertain significance
rs100999023412:81,799,585C/Auncertain significance
rs52905074612:81,799,621G/Auncertain significance
rs126339009212:81,799,625C/Tuncertain significance
rs75583418012:81,839,440C/Tlikely benign
rs1242672512:81,843,128G/Aintron variant
rs52900354812:81,868,060C/G
rs255154268312:82,070,595G/Auncertain significance
rs20092549212:82,070,607G/Cuncertain significance
rs104033482512:82,070,617C/Tuncertain significance
rs54095144412:82,070,622T/Cuncertain significance
rs3450323912:82,124,199G/Tintron variant
rs255177761312:82,147,786G/Auncertain significance
rs37007371912:82,147,858G/Cuncertain significance
rs77586856812:82,147,871G/Auncertain significance
rs124124519512:82,147,946C/Guncertain significance
rs76898565212:82,147,961G/Cuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.